Giant Craniospinal Intramedullary Neurenteric Cyst in Infant-Case Report and Review of Literature.
BACKGROUND
Neurenteric cysts are rare congenital lesions derived from an anomalous connection between the primitive ectoderm and endoderm.


CASE DESCRIPTION
A 2-month-old infant presented with an insidious onset of upper limb weakness. Magnetic resonance imaging of the spine revealed a contrast-enhancing solid mass located anterior to the spinal cord at the level of the cervicothoracic junction, which was isointense on T1-weighted images and hyperintense on T2-weighted images. The lesion was associated with marked spinal cord compression and also with a giant intramedullary cyst that extended proximally into the cranium. Spinal dysraphism was noted. The patient underwent cervicothoracic laminotomy, drainage of the cyst contents, and a complete excision of the solid component. Neurologic function recovery was observed postoperatively.


CONCLUSIONS
We report and discuss the clinical presentation, pathogenesis, and neuroradiologic findings in an infantile case of a giant craniospinal intramedullary neurenteric cyst. Early recognition is beneficial because of its benign nature and good clinical outcome following total surgical resection.
['Diyora|Batuk|B|', 'Bhende|Bhagyashri|B|', 'Kukreja|Sanjay|S|']
D002574:Cervical Vertebrae D003937:Diagnosis, Differential D006801:Humans D007223:Infant D008297:Male D009436:Neural Tube Defects D013117:Spinal Cord Compression D016135:Spinal Dysraphism D016896:Treatment Outcome
Neurenteric cyst Spinal dysraphism Enterogenous cyst Intraspinal cyst Spinal cord tumor