Congenital fulminant Kaposiform hemangioendothelioma of the leg.
Kaposiform hemangioendothelioma is a rare locally aggressive vascular tumor associated with Kasabach Merritt syndrome. We present a case of congenital Kaposiform hemangioendothelioma of the leg in a female infant who was born to a mother treated with various medications including etanercept, a TNF antagonist, due to rheumatoid arthritis. The neonate suffered from a fulminant form of Kasabach Merritt syndrome with disseminated intravascular coagulation (DIC) resulting in multi-organ failure which led to her demise.
['Ergaz|Zivanit|Z|', 'Bar-Oz|Benjamin|B|', 'Vainer|Gilad W|GW|', 'Abu-Leil|Sinan|S|', 'Simanovsky|Natalia|N|', 'Diav-Citrin|Orna|O|']
D005260:Female D006390:Hemangioendothelioma D006801:Humans D007231:Infant, Newborn D059885:Kasabach-Merritt Syndrome D007866:Leg D012514:Sarcoma, Kaposi
Congenital Kaposiform hemangioendothelioma Kasabach Merritt syndrome Etanercept Multi-organ failure