The prenatal diagnosis of a rare circular shunt with absent pulmonary valve syndrome.
Absent pulmonary valve syndrome (APVS) with tricuspid atresia is very rare. We report a case of APVS in which the fetus died due to severe hydrops fetalis. In addition to weakened cardiac contraction due to left ventricular noncompaction cardiomyopathy, a circular shunt through a ventricular septal defect exacerbated heart failure. Although APVS with tricuspid valve atresia is not supposed to cause a circular shunt, we herein present the echocardiographic demonstration of a case of circular shunt.
['Inamura|Noboru|N|https://orcid.org/0000-0002-6270-1158', 'Takada|Nori|N|', 'Marutani|Satoshi|S|']
prenatal diagnosis circular shunt pulmonary valve hydrops fetalis echocardiography