Nutrition Management of Cystic Fibrosis in the 21st Century.
Despite significant advancements made in life expectancy over the past century, cystic fibrosis remains a life-threatening genetic disease that affects the gastrointestinal tract, and it has significant impact on the nutrition status of those with the disease. Nutrition management includes a high-calorie/high-fat diet, pancreatic enzyme replacement therapy, vitamin and mineral replacement, and enteral support as needed. As patients are living longer, clinicians may encounter patients with cystic fibrosis in obstetrician offices, endocrine clinics, or hospital settings, owing to lung transplantation or for treatment for distal intestinal obstruction syndrome.
['Schindler|Teresa|T|', 'Michel|Suzanne|S|', 'Wilson|Alexandra W M|AW|']
D003550:Cystic Fibrosis D003920:Diabetes Mellitus D059305:Diet, High-Fat D002149:Energy Intake D004750:Enteral Nutrition D010188:Exocrine Pancreatic Insufficiency D005260:Female D005765:Gastrointestinal Agents D006801:Humans D007415:Intestinal Obstruction D016040:Lung Transplantation D008297:Male D044342:Malnutrition D009752:Nutritional Status D010194:Pancreatin D011247:Pregnancy D011248:Pregnancy Complications D014815:Vitamins
cystic fibrosis diabetes mellitus exocrine pancreas insufficiency lung diseases nutrition therapy pancreas