Adult-onset Still's disease with prominent polyserositis.
Adult-onset Still's disease is a systemic autoinflammatory disease the presentation of which can often mimic infection. As a consequence, there is often a delay in diagnosis. Serositis is a recognised but less common clinical feature that can result in complications including cardiac tamponade and constrictive pericarditis. We describe a case of adult-onset Still's disease without the hallmark rash or significant arthritis, presenting with polyserositis that showed a good response to initial steroid treatment and sustained remission with anakinra. An elevated procalcitonin level was due to active adult-onset Still's disease, not bacterial infection.
['Farooq Sheikh|Ali Sibtain|AS|', 'Marks|Jonathan|J|', 'Hopkinson|Neil|N|']
D000893:Anti-Inflammatory Agents D018501:Antirheumatic Agents D005260:Female D006801:Humans D053590:Interleukin 1 Receptor Antagonist Protein D008875:Middle Aged D010490:Pericardial Effusion D016706:Still's Disease, Adult-Onset D016896:Treatment Outcome
pericarditis Adult-onset Still’s disease anaemia pleural effusion pyrexia of unknown origin