IgG4-Related Sclerosing Cholangitis: A Clinical and Imaging Review.
OBJECTIVE. The purpose of this article is to present the pathologic and clinical features of IgG4-related sclerosing cholangitis (ISC), illustrate the associated imaging findings, and discuss treatment of the disorder. CONCLUSION. ISC is an inflammatory disorder involving the biliary system and resulting in strictures. Although often associated with autoimmune pancreatitis, it may be an isolated disease. Differentiation of ISC from other forms of cholangitis and cholangiocarcinoma is difficult but necessary for management. Imaging is important in diagnosing and assessing the extent of disease and planning a management strategy.
['Madhusudhan|Kumble S|KS|', 'Das|Prasenjit|P|', 'Gunjan|Deepak|D|', 'Srivastava|Deep N|DN|', 'Garg|Pramod K|PK|']
D001327:Autoimmune Diseases D001650:Bile Duct Neoplasms D001653:Bile Ducts, Intrahepatic D018281:Cholangiocarcinoma D015209:Cholangitis, Sclerosing D003937:Diagnosis, Differential D006801:Humans D007074:Immunoglobulin G D010195:Pancreatitis
IgG4-related sclerosing cholangitis sclerosing cholangitis autoimmune pancreatitis IgG4-related disease primary sclerosing cholangitis