Anterior skull base duplication requiring delivery via EXIT procedure: A case report.
Duplication of the anterior skull base structures is an extremely rare malformation of failed midline blastogenesis. We present the case of a child with an obstructive oral cavity mass diagnosed on prenatal imaging. The child was successfully delivered by EXIT procedure, a tracheotomy was performed, and postnatal imaging demonstrated an array of craniofacial malformations, including complete duplication of the maxilla, pituitary glands, aqueducts of Sylvius, and basilar arteries. The child underwent excision of the duplicate maxilla, resulting in a wide cleft palate that will be repaired at a future date.
['Shires|Courtney B|CB|', 'Giurintano|Jonathan P|JP|', 'McLevy-Bazzanella|Jennifer|J|', 'Thompson|Jerome|J|']
D000015:Abnormalities, Multiple D001488:Basilar Artery D002535:Cerebral Aqueduct D002648:Child D019465:Craniofacial Abnormalities D036861:Delivery, Obstetric D005260:Female D006801:Humans D008437:Maxilla D010902:Pituitary Gland D019291:Skull Base D014140:Tracheotomy D016216:Ultrasonography, Prenatal
EXIT Procedure Airway