A fatal case of primary cutaneous gamma-delta T-cell lymphoma complicated by HLH and cardiac amyloidosis.
Gamma-delta T-cell lymphomas (GD-TCL) are rare and rapidly fatal neoplasms that are often associated with Hemophagocytic Lymphohistiocytosis (HLH), a syndrome of fevers, cytopenias, and multiorgan failure that often leads to a rapid death. We report the first case demonstrating an association between GD-TCL, HLH, and cardiac amyloidosis, presenting a novel mechanism for rapid deterioration in these patients.
['Gibson|Juliet Fraser|JF|', 'Kapur|Lucy|L|', 'Sokhn|Joseph|J|', 'Xu|Mina|M|', 'Foss|Francine M|FM|']
Amyloidosis hemophagocytic lymphohistiocytosis cutaneous T-cell lymphoma gamma–delta primary cutaneous gamma–delta T-cell lymphoma