Etiology and outcome of XXXX managed at an Australian liver transplant unit.

@entity1 @entity879 @entity4968 @entity1443 @entity99
BACKGROUND AND AIMS: The primary aims were to identify the incidence, etiology and outcome of all adult cases of @entity879 ( @entity879 ) presenting to the Victorian Liver Transplant Unit over the 14 year period since the Unit was established in 1988. METHODS: The database of the Unit was used to identify all adult @entity1 (>16 years) who were referred to the Austin and Repatriation Medical Center in Melbourne with @entity879 between 1988 and 2001. The Austin and Repatriation Medical Center is the sole provider of adult liver transplantation services for the states of Victoria and Tasmania. RESULTS: 80 @entity1 (64 female, 14 male) with @entity879 were referred, at a rate of approximately one case per million population per year. The mean age was 37.6 +/- 13.7 years. Most cases were due to either @entity1443 @entity4968 n = 29 (36%) or non-A non-B (idiopathic) @entity99 n = 27 (34%). Thirty-five @entity1 were listed for transplantation, of which 26 underwent the procedure (77% of transplantation @entity1 currently alive). Nine @entity1 were listed for transplantation but did not undergo the procedure, eight died before a donor became available and one recovered. Of the 30 @entity1 who survived without transplantation, 20 cases were due to @entity1443 @entity4968 . CONCLUSIONS: Liver transplantation has had a major impact on survival of @entity1 with @entity879 , most significantly in @entity1 with @entity879 due to causes other than @entity1443 @entity4968 , in whom survival without transplantation is uncommon. Survival in those who undergo transplantation for @entity879 is excellent, but a significant percentage of @entity1 listed for transplantation die before a donor organ becomes available.
