Aberrant tendinous chords with tethering of the tricuspid leaflets: a congenital anomaly causing severe XXXX .

@entity1 @entity997 @entity4924
OBJECTIVE: To define the entity of @entity997 caused by tethering of the tricuspid valve leaflets by aberrant tendinous chords. DESIGN: Retrospective study. SETTING: Tertiary care centre (university teaching hospital). @entity1 : 10 @entity1 with unexplained severe @entity997 . METHODS: The last 13 500 echocardiographic studies from our facility were reviewed to identify @entity1 with severe unexplained @entity997 . Tethering was defined by the presence of aberrant tendinous chords to the tricuspid valve leaflets limiting the mobility of the tricuspid leaflet and resulting in incomplete coaptation and apical displacement of the regurgitant jet origin. Aberrant tendinous chords were defined as those inserting at the clear zone of the tricuspid leaflet and not originating from the papillary muscle. @entity1 fulfilling the diagnostic criteria for @entity4924 were excluded. RESULTS: 10 @entity1 with aberrant tendinous chords tethering one or more tricuspid valve leaflets were identified. There were short non-aberrant tendinous chords in seven @entity1 , five of whom also had right ventricular or tricuspid annulus dilatation. CONCLUSIONS: Tethering of the tricuspid valve leaflets by aberrant tendinous chords can be the sole mechanism of @entity997 . It is often associated with short non-aberrant tendinous chords, which may develop secondary to right ventricular or tricuspid annulus dilatation. Awareness of tethering as a cause of @entity997 may be important in planning reconstructive surgery.
