Three cases of XXXX in Fontan patients: Review of the literature and suggestions for hepatic screening.

@entity157 @entity82 @entity101 @entity450
UNASSIGNED: The Fontan procedure has been used since 1971 as a palliative treatment for various (functionally) univentricular hearts. The systemic venous blood flows passively to the pulmonary arteries, without passing through a functional ventricle. This results in chronic @entity450 , which may lead to liver @entity82 , @entity82 and @entity157 . This review discusses possible screening modalities for liver @entity82 and @entity82 in the Fontan population and proposes a screening protocol. We suggest starting screening for progression of @entity82 and @entity82 in collaboration with the hepatologist circa 10years after Fontan completion. The screening programme will consist of a yearly evaluation of liver laboratory tests in conjunction with imaging of the liver with ultrasound or MRI every two years. In case of liver @entity82 or @entity82 , (reversible) causes should be ruled out (e.g. obstruction in the Fontan circuit). In case of severe @entity82 or @entity82 , other complications of portal @entity101 should be evaluated and screening for @entity157 is required on a regular (6-12months) basis. As regards @entity157 , treatment should be discussed in a multidisciplinary team, before deciding a treatment modality.
