[Treatment of XXXX with limb preservation. A case report and review of the literature].

@entity7197 @entity1567 @entity5 @entity9530 @entity158 @entity1155 @entity85
BACKGROUND: @entity7197 is a rare lesion of low-grade malignancy, and represents 1% of @entity5 of bones, and is mainly located in two regions of the body, jaw ( @entity1567 ), and lower extremities. The treatment of choice is surgery due to it being a radio- and chemotherapy-resistant @entity5 . CLINICAL CASE: A 39 year old male with a history of neonatal hydrocephalus with moderate @entity1155 . He began with @entity158 in the posterior region of the left thigh for one year before admission, which was managed as @entity9530 . He had sudden intense @entity158 on walking, that led him to fall over. In the examination, left pelvic limb with @entity85 in the distal third with increase in volume in the thigh, with @entity158 to palpation, and presence of crackles in the distal third of the femur. A biopsy of the thigh was performed, with subsequent local wide excision + replacement of bone with cadaver bone and a central medullary nail. The final diagnosis was @entity7197 . CONCLUSION: The @entity7197 are rare @entity5 . It is important to recognise this type of @entity5 from the beginning, since its prognosis is excellent in initial stages. It is important to have free margins as survival is very high.
