Successful treatment of chronic lower respiratory tract @entity281 by macrolide administration in a XXXX with intralobar pulmonary sequestration and primary @entity910 .

@entity1 @entity5409 @entity1353 @entity18697 @entity4581 @entity409 @entity794 @entity910 @entity281 @entity358 @entity74 @entity1729 @entity1345
@entity910 ( @entity910 ) is a @entity74 associated with abnormalities in ciliary structure and function. Although recurrent @entity1729 associated with @entity409 is a common clinical feature, there is no standardized treatment or management of @entity1729 in @entity910 @entity1 . Here, we report that @entity1729 with @entity910 and @entity18697 ( @entity18697 ) were treated successfully with @entity4581 before the surgical resection of @entity18697 . A 15-year-old non-smoking Japanese @entity1 was admitted for productive cough and @entity1353 on exertion. Chest CT scan on admission showed complex cystic LESIONS with air-fluid level in the right lower lobe, and diffuse nodular shadows in the whole lobe of the lung. On flexible bronchoscopy examination, sputum and bronchiolar fluid cultures revealed @entity794 ( @entity794 ). An electron microscopic examination of the cilia showed inner @entity1345 . Administration of @entity4581 improved the lower respiratory tract @entity281 associated with @entity794 . CT angiography after @entity4581 treatment demonstrated an aberrant systemic artery arising from the celiac trunk and supplying the @entity5409 that were incorporated into the normal @entity358 without their own pleural covering. Based on these results, the @entity1 was diagnosed with @entity910 and @entity18697 . Because of the @entity4581 treatment, resection of the @entity18697 was performed safely without any complications. Although further observation of @entity4581 treatment is needed, we believe that @entity4581 may be considered one of the agents for treating @entity910 .
