Presenting features of XXXX .

@entity1 @entity2749 @entity6 @entity341 @entity4053 @entity1270 @entity413
Idiopathic @entity4053 (IKH) is an important cause of emergent @entity4053 among @entity1 . We present a case series of 24 @entity1 with IKH in an effort to provide a current clinical description of this disorder. Secondly, we provide a crude lower-bound estimate of the incidence of IKH in an @entity341 ( @entity341 ) setting. The charts of 94 non- @entity6 @entity1 presenting to an @entity341 during a period of 64 months with a diagnosis of @entity4053 as identified via ICD-9 codes were reviewed. Eleven @entity1 , accounting for 24.4% of all significant @entity2749 unrelated to @entity6 in @entity1 over 6 months of age, were diagnosed with IKH. These @entity1 accounted for 31.4% of @entity2749 among previously heathy @entity1 older than 6 months. A further review of 13 individuals with IKH identified from an endocrinology specialty clinic was also performed. Among all 24 individuals identified with IKH, the mean age of presentation was 30.8 months. We have found IKH to be the most common cause of @entity4053 among previously healthy @entity341 @entity1 during childhood. In our series, @entity1 with IKH presented initially before 5 years of age with symptomatic @entity4053 during the morning hours after a moderate fast. These @entity1 were found to have @entity1270 with symptoms resolving after @entity413 administration. @entity1 with IKH were more likely to be Caucasian, male gender, and have a low body weight.
