[Experience of 76 cases of XXXX , clinical diagnosis and treatment].

@entity1 @entity8468 @entity600 @entity1274 @entity393 @entity258
OBJECTIVE: To explore the disease incidence, clinical symptoms, prevention and treatment measures of the @entity8468 ( @entity8468 ). METHOD: Retrospective analyse the medical history, hearing, vestibular function examination and treatment of 76 @entity8468 @entity1 who were diagnosed in our department of Otolaryngology from 2002 to 2008. RESULT: Most @entity1 (93.4%) showed @entity1274 . Part of @entity1 (61.8%) showed air-bone conduction gap in low frequency. The @entity393 of 43 ears is > 40-60 dB HL, > 60 -80 dB HL 47 ears, > 80 dB HL 62 ears. Decline curve is the characteristic of the Audiogram. The decline in high-frequency 112 ears, flat curve in 29 ears, island hearing in 11 ears. Forty-six @entity1 were conducted the vestibular function examination, which showed @entity258 . Tympanogram showed that 141 ears are type A, 11 ears are type C. High-resolution CT scan revealed that @entity8468 minimum diameter is 2.2 mm and the largest is 6.2 mm, with a wide opening and deep narrower, and showed the "triangle" or "flared". Forty-two cases of this group were simple dilatation of the @entity8468 , and no large vestibular semicircular canal @entity600 or @entity600 . There was no intellectual and other development disorders. In accordance with the degree of @entity393 , 20 cases of @entity1 restored hearing after drug treatment. Eleven were cases fit a suitable hearing aid and carried out the language rehabilitation training. Forty-five very severe @entity1 were implanted the cochlear and mapping one month later. CONCLUSION: Fluctuative and progressive @entity393 is the main clinical symptoms of @entity8468 . The @entity1 should be examined by high resolution CT scan of the temporal bone. There is no precise and effective treatment for the disease. It is very important for the deaf @entity1 who have residual hearing to fit hearing aids and carry out the language rehabilitation training as soon as possible. As for the @entity1 who suffer from @entity393 severely and the hearing aid cannot achieve effective compensation, the cochlear implant should be considered.
