[Maxillary bone XXXX ].

@entity1 @entity2253 @entity39 @entity2133 @entity4 @entity17795 @entity2883 @entity370 @entity378
INTRODUCTION: @entity370 is an unexplained systemic @entity2883 . Bone localizations of the disease are rare. We report a maxillary localization. CASE: A 35-year-old @entity1 consulted for facial dysmorphia first observed 2 years before. This swelling was associated to @entity17795 lesions and @entity2133 . The facial asymmetry was due to maxillary gingival and @entity4 . It was associated with scarring in the legs and a purple nodular facial lesion. Lip and jaw biopsies revealed @entity2253 without @entity39 . The panoramic dental X-ray showed diffuse horizontal alveolar ridge lysis and CT scan revealed an osteolytic lesion of the right maxilla associated to a bone-condensing lesion of the left hemi-mandible. DISCUSSION: The diagnosis of @entity370 is made in case of @entity2253 without @entity39 and the ruling out of other possible diagnoses, including @entity378 . Bone involvement is rare; face and maxillary localization are extremely rare. The recommended treatment is corticosteroids. Facial remodeling surgery is not recommended.
