XXXX as a cause of @entity120 in adults.

@entity1 @entity154 @entity3657 @entity1353 @entity120 @entity8577 @entity1163 @entity3297
@entity3657 ( @entity3657 ) is an underrecognized condition in the adult population. @entity3657 can lead to @entity120 but is likely misdiagnosed as either @entity8577 or chronic @entity120 . We retrospectively identified adult @entity1 with @entity3657 either in its isolated form or related to other @entity154 from January 1998 to September 2012. We reviewed the @entity1 ' clinical data by using our hospital electronic medical records and/or their paper charts. We identified 6 adult @entity1 with @entity3657 with an age range of 16-56 years (1 @entity1 and the rest @entity1 ). Presenting signs and symptoms were thoracic murmurs, progressive @entity1353 , and @entity1163 . Three @entity1 had @entity3297 . Pulmonary angiography showed that @entity3657 was predominantly located in main branches or lobar pulmonary arteries in 5 @entity1 , while in 1 @entity1 the arterial narrowing was at the level of the segmental pulmonary arteries. Right heart catheterization showed a mean pulmonary artery pressure (PAP) ranging from 35 to 60 mmHg. Balloon dilation was performed in all @entity1 , predominantly in the lobar arteries, and it caused a decrease in mean PAP that ranged from 16% to 46% in 5 @entity1 . In 1 @entity1 the mean PAP did not decrease. All but 1 @entity1 had follow-up echocardiograms at 1 year that showed stable echocardiographic findings. @entity120 due to @entity3657 continues to presents a diagnostic challenge. Therefore, a high index of suspicion during the initial evaluation of @entity120 is essential for its prompt diagnosis and adequate treatment.
