XXXX : report of seven cases and review of English literature.

@entity1 @entity5 @entity6687 @entity253 @entity255
@entity253 is rare. Before 1993, there were only 21 cases reported in the English literature. This article reports our experience in managing this disease and reviews experiences from recent English literature. A retrospective review of @entity1 with @entity253 was conducted in our institution. A search of the English literature between 1993 and 2002 was performed in the MEDLINE database using " @entity253 " as the keyword. Seven @entity1 with @entity253 were treated in our hospital. Another 50 cases were reported in the recent literature. This amounted to a total of 78 cases so far reported. The male to female ratio was approximately 2 : 1. The mean age at presentation was 63 years. Most @entity1 presented typically with @entity255 . Malignant change was present in 33 @entity1 (42%). Concomitant @entity6687 was noticed in 33 @entity1 (42%). The overall resection rate was 55%. The mean survival was 28 months following resection, irrespective of histological type. @entity1 without @entity5 resection had a poorer survival of less than 11 months. @entity253 presents typically with @entity253 and it occurs most often in elderly males. Resection is recommended because of the considerable malignancy rate, diffuse pattern of disease, and better survival following curative surgery. Malignant histology is not always associated with a poorer prognosis provided that radical resection can be achieved.
