[ XXXX : too often detected too late? A contribution to early diagnosis of @entity9465 ].

@entity1 @entity32 @entity16892 @entity1036 @entity409 @entity262 @entity2319 @entity393 @entity9465 @entity394 @entity3170 @entity288
BACKGROUND: @entity9465 is an uncommon disease characterized by @entity32 , @entity409 and symptoms of @entity262 . The etiology is unknown, however there is evidence for an autoimmune pathogenesis. The "typical" @entity9465 presents as bilateral @entity16892 . The presence of other inflammatory manifestations in addition of @entity1036 has been termed as "atypical" @entity9465 . @entity1 : We report on six @entity1 presenting with typical as well as atypical ocular manifestations between 1982 and 1994. Typically, the illness was accompanied by systemic symptoms. Each @entity1 had audiovestibular involvement, that was the initial presentation in 4 cases. @entity394 often preceded @entity393 . Five of our @entity1 not only presented with @entity1036 but also demonstrated signs of @entity32 diagnosed as @entity3170 or @entity3170 . In two @entity1 these ocular symptoms were the first signs of @entity9465 , recurred periodically and did not respond to corticosteroids. RESULTS: In 3 @entity1 that were diagnosed early and treatment with @entity288 was initiated early, hearing could be stabilized, in the remaining @entity1 @entity2319 could not be prevented. CONCLUSION: The importance of being aware that @entity409 may occur in @entity1 with @entity32 , and the fact that early immunotherapy may prevent the risk of @entity2319 , has to be emphasized.
