Histologic variability and diverse oncologic outcomes of XXXX .

@entity1 @entity2828 @entity263 @entity1069 @entity242 @entity5 @entity1352 @entity420 @entity3 @entity674 @entity980 @entity2483 @entity1821
PURPOSE: Primary @entity1069 are a rare type of @entity263 that account for less than 0.1% of primary @entity1069 . We analyzed the experience of a single institution with @entity1069 over 20 years. MATERIALS AND METHODS: In this case series, the medical records of 20 @entity1 with @entity1069 were reviewed from June 1990 to December 2013 to identify symptoms at presentation, diagnostic procedures, @entity3 presence and development, histologic subtype, French F  d  ration Nationale des Centres de Lutte Contre le @entity5 grade, primary @entity5 grade and size, and treatment sequence, including surgery and preoperative and postoperative therapies. The average follow-up period was 23.6 months (range, 1.4-83.3 months). RESULTS: The average @entity1 age was 46.3  16.7 years. Most @entity1 presented with lower urinary tract symptoms (55%). The histologic subtype was spindle cell @entity242 in five @entity1 (25%), @entity980 in three @entity1 (15%), @entity1352 in three @entity1 (15%), @entity1821 in three @entity1 (15%), @entity674 in three @entity1 (15%), and @entity2828 , nerve @entity5 , and @entity420 with @entity2483 (5% each). For @entity1821 , two @entity1 were alive after complete surgical resection and had a good prognosis. At last follow-up, 15 @entity1 had died of @entity242 . The 2- and 5-year actuarial survival rates for all 20 @entity1 were 53% and 12%, respectively (medial survival, 20 months). CONCLUSIONS: The disease-specific survival rate of @entity1069 is poor. However, @entity242 that is detected early shows a better result with proper management including surgical intervention with radio-chemotherapy than with no treatment. Early diagnosis and complete surgical resection offer @entity1 the best curative chance.
