Clinical Features of XXXX : A Report on a Nationwide Multicenter Study in Japan.

@entity1 @entity5 @entity649 @entity358 @entity1576 @entity85 @entity105 @entity9129
UNASSIGNED: Aim   The current study aimed to assess the perinatal risk of @entity9129 ( @entity9129 ) and to establish a suitable surgical strategy in consideration of postoperative lung growth and problems during adulthood. Methods   Among 874 @entity9129 @entity1 identified in a nationwide survey, 428 @entity1 were born between 1992 and 2012 and treated at 10 high-volume centers were retrospectively reviewed with statistical analysis. Results   In the 194 @entity1 who were prenatally diagnosed to have @entity9129 , 16.7% presented with fetal hydrops as observed using ultrasonography. The Apgar score (5 minutes) was lower than 5 in 5.4%. As of postnatal day 30, 14.0% of the neonatal @entity1 required respiratory support, and 3.3% (8/243) had died because of @entity358 . Among those who were asymptomatic immediately after birth, 33.6% of the @entity1 developed the @entity1576 during their first year of life, and 22.1% did so between the age of 1 and 2 years. The postoperative percent vital capacity among the prenatally diagnosed @entity1 was significantly higher than that among the postnatally diagnosed @entity1 (98.3        11.9 vs. 81.7        9.7, p   <   0.0222). Late complications included @entity85 in 30 @entity1 and persistent @entity358 in 4 @entity1 , whereas @entity5 was not observed in the present series. Conclusions   Approximately 10 to 15% of prenatally diagnosed @entity9129 @entity1 may carry a high risk of perinatal @entity649 . Early operation before developing episodes of @entity358 , seem to be associated with a better development of the reserved lung during later life. The incidence of @entity105 among @entity1 with @entity9129 may be extremely low.
