[Primary XXXX . Case report and review of the literature].

@entity1 @entity697 @entity5 @entity189 @entity420 @entity70976 @entity1487
A rare case of primary @entity420 (less than 250 cases described in the literature) in a 36 year-old female @entity1 presenting signs and symptoms of an @entity697 is reported. @entity189 of the vermiform appendix is a rare @entity5 of the gastrointestinal tract with an incidence of about 0,01-0,2%. Usually the diagnosis of @entity420 is difficult because symptoms and signs are not pathognomonic. In the case described, the diagnosis was intra and postoperative and confirmed by the pathological examination of the surgical specimens. At laparotomy, performed under suspicion of an @entity697 , disseminated disease was discovered, characterized by the involvement of the two ovaries, the left colon, the cecum, the vermiform appendix, with a peritoneal carcinosis and a hydroureteronephrosis. According to the dissemination of the disease, the surgical treatment was right hemicolectomy, anterior resection of left colon, bilateral oophorectomy and omentectomy. The post-operative course was regular. Adjuvant therapy was performed for 6 cycles, with @entity1487 and @entity70976 . The @entity1 is still alive after 6 months and there is no sign of progression of the disease. A mild left hydroureteronephrosis is persistent.
