Significance of the residual XXXX in multistage repair of @entity1699 .

@entity1 @entity308 @entity1699 @entity338 @entity2333 @entity943
OBJECTIVE: The population of @entity1 who received right ventricle-to-pulmonary artery shunt (RV-PA) at Norwood procedure (NP) is growing, but limited data are available regarding the long-term outcome. The aim of this study was to present operative outcomes and mid-term hemodynamics and to assess the impact of the residual @entity2333 on the results in @entity1 undergoing three-staged surgery with RV-PA application at NP. METHODS: Between June 2001 and June 2009, 229 @entity1 with @entity1699 ( @entity1699 ) and variants underwent NP with RV-PA; 172 have proceeded to stage II and 95 to stage III. The medical records (clinical data, echocardiographic records, cardiac catheterization reports, electrocardiograms, and surgical notes) were retrospectively reviewed. RESULTS: The later era of NP was associated with significantly better outcome (2001-2004: 1- and 5-years' survival were 64.3% and 59.8%, respectively; 2005-2009: 1- and 4-years' survival were 93.1% and 86.9%, respectively) (p<0.001). There was no association between long-term survival and diagnosis ( @entity1699 / @entity1699 variant) (p=0.39). The incidence of @entity308 and moderate or severe systemic @entity338 among the @entity1 who required balloon aortoplasty (BA) before stage II surgery was significantly higher than in @entity1 without aortic arch obstruction (p=0.027, p=0.008, respectively). In midterm follow-up, BA had no significant influence on the actuarial survival (p=0.089). No @entity943 were noticed at any stage. CONCLUSIONS: The RV-PA shunt is a safe technique that does not seem to impair systolic or electrical ventricular function; its outcomes continue to improve with growing experience. Combined cardiologic interventional and surgical procedures are required to optimize the outcomes.
