Power stapes: an alternative method for treating XXXX in @entity6926 ?

@entity1 @entity8719 @entity389 @entity954 @entity393 @entity6926
OBJECTIVE: To present power stapes, stapedotomy, and middle ear implantation with Vibrant SoundBridge (VSB) performed in a one-step surgery as an alternative option for hearing rehabilitation in @entity1 with @entity6926 ( @entity6926 ). STUDY DESIGN: Retrospective case series. SETTING: Tertiary referral ear center. @entity1 : A family with genetically proven @entity6926 Type I. INTERVENTIONS: Two @entity1 , mother and son, with severe to profound mixed @entity393 underwent 3 power stapes, 1 unilateral and 1 bilateral sequential. MAIN OUTCOME MEASURES: Thorough audiological diagnostic batteries including aided and unaided pure-tone and free-field audiometry and Freiburg monosyllabic word test were used to assess the preoperative status and the postoperative hearing outcome. High-resolution computed tomography of the temporal bones was performed as well. Surgical procedure and any special considerations were analyzed in detail. RESULTS: The hearing outcome was favorable in all cases, showing in comparison to the preoperative values an average improvement of 36.8 dB. Severe @entity954 of the middle ear mucosa was the only complication and could be easily controlled by allowing short time intervals. @entity389 did not occur in any case. CONCLUSION: Power stapes represents a safe and promising procedure for treating @entity393 in selected @entity1 with @entity6926 . Furthermore, it introduces a new, advantageous VSB application in cases of mixed @entity393 with severe @entity8719 and increased bone-conduction thresholds.
