[Combined periampullary adenocarcinoma and XXXX in type 1 @entity4786 : report of one case].

@entity1 @entity1087 @entity353 @entity8799 @entity5 @entity189 @entity74 @entity4786 @entity221 @entity674
@entity4786 is a hereditary @entity74 with high rates of de novo mutations, and carries a high risk of @entity5 . It affects both sexes and all races and ethnic groups. It is characterized by multiple cutaneous lesions and @entity5 , both benign and malignant, especially in the nervous system. We report a 52-year-old @entity1 with a type 1 @entity4786 , presenting with @entity221 , @entity1087 and @entity353 . On physical examination, the @entity1 was @entity1087 and had "caf   au lait" spots in the skin. A magnetic resonance imaging showed bile duct dilation and a possible @entity189 . The @entity1 was operated, during the exploration she presented a @entity5 and multiple small nodular lesions in the stomach, the @entity5 was resected with a pancreaticoduodenectomy and the nodular gastric lesions were biopsied. The pathological study revealed a combined @entity8799 . The study of the stomach lesions revealed a @entity674 . Four months after surgery, the @entity1 is in good condition.
