Incidence and Survival of Primary XXXX in the United States.

@entity1 @entity1489 @entity241 @entity242
BACKGROUND: @entity241 ( @entity241 ) is a rare @entity242 for which data on risk factors, incidence, and survival are limited. OBJECTIVE: The authors sought to establish a comprehensive report on the incidence of and survival from primary @entity241 . METHODS: The authors used data from the 18 registries of the Surveillance, Epidemiology, and End Results Program from 2000 to 2010. RESULTS: Overall incidence was 4.1 per million @entity1 -years and steady over the decade. Trunk was the most common anatomic site except in older @entity1 . Incidence among @entity1 was 1.14 times higher than @entity1 (95% confidence interval [CI] of rate ratio: 1.07-1.22). Incidence among blacks was almost 2 times the rate among whites (95% CI of rate ratio: 1.8-2.1). Ten-year relative survival of @entity241 was 99.1% (95% CI: 97.6-99.7). Increased age, male sex, black race, and anatomic location of the limbs and head as compared with the trunk were associated with higher all-cause mortality. CONCLUSION: This is the largest population-based study of @entity241 derived from a cohort of almost 7,000 @entity1 . The epidemiologic profile of @entity241 differs from most @entity1489 . Incidence is stable and highest among @entity1 and blacks. Worse survival is associated with increased age, male sex, black race, and anatomic location of the limbs and head.
