[A case of XXXX after reconstruction of an @entity1028 associated with Beh  et's disease and special reference to 95 reported cases in Japan].

@entity1 @entity834 @entity2009 @entity449 @entity439 @entity158 @entity1028
A 45-year-old male with incomplete type of Beh  et's disease was operated on because of @entity1028 . The post-operative course was uneventful. On twenty-one months after discharge, the @entity1 noticed left @entity158 and tarry stool, and was referred to our hospital. Computed tomography and angiography showed @entity2009 at the proximal aortic @entity834 site. Aortic reconstruction was performed, but the @entity1 died on 36th post-operative day. We analysed the reports of 95 cases of @entity439 associated with vasculo-Beh  et's disease in Japan. This series comprised 82 @entity1 , 9 @entity1 and 4 unknowns. The cases were classified to four groups, which were incomplete type (48 cases), complete type (27 cases), suspected type (12 cases) and unknown (8 cases). They had 46 @entity439 . Operation was performed on 29 @entity449 and 73 peripheral @entity439 . Eleven @entity449 and twelve peripheral @entity439 had @entity834 complication post-operatively. Four cases after reconstruction of @entity1028 was complicated with @entity2009 . They were all dead post-operatively. Vasculo-Beh  et's disease with @entity449 is comparatively a rare entity and morbidity and mortality is high because of its etiological characteristics.
