En-bloc resection of a XXXX : a case report and review of the literature.

@entity1 @entity362 @entity5 @entity490 @entity158 @entity1282 @entity1821
BACKGROUND: @entity362 are an extremely rare condition with only 17 cases described in the literature since 1980. They can reach enormous size and cause significant abdominal symptoms. The most important differential diagnosis is the well-differentiated @entity1821 , which preoperatively often may not definitely be ruled out. CASE PRESENTATION: We present the case of a 73 year-old Caucasian @entity1 with a @entity362 of 9 kg measuring 55 cm in diameter. The @entity1 presented with @entity490 and swelling that had been slowly progressive for the last 15 years. On computerized tomography an immense @entity5 was revealed. Intraoperatively, the @entity5 did not show any signs of infiltrative growth, therefore sole @entity5 extirpation was performed. CONCLUSION: @entity362 are not clearly distinguishable from well-differentiated @entity1821 on imaging and even biopsies may be misleading. Moreover, abdominal symptoms, i.e. @entity158 , obstipation and @entity1282 may occur due to mechanical displacement. Therefore, surgical exploration with complete oncological resection is the therapy of choice if malignity cannot be ruled out.
