XXXX : a rare @entity5 with a particular clinical and paraclinical presentation.

@entity1 @entity788 @entity5409 @entity39 @entity5 @entity1066 @entity3981 @entity420 @entity292 @entity715 @entity1412 @entity360
@entity3981 ( @entity3981 ) of the @entity788 is a rare @entity5 with an extremely low incidence rate. While the number of reported @entity1 with @entity3981 is relatively small, a long-term survival rate has been noted in @entity1 with neuroendocrine differentiation. A 39-year-old @entity1 visited our emergency department for @entity360 . Endoscopy indicated extrinsic compression of the posterior body of the stomach, together with a large, 10-cm, central @entity1066 covered with @entity39 tissue. Abdominal computed tomography (CT) indicated a lesion that involved the whole of the @entity788 , with a @entity292 in the stomach, which was suspected of being a @entity5 of the @entity788 . Magnetic resonance imaging (MRI) of the @entity788 was performed, and the results further strengthened our suspicions by demonstrating the presence of @entity5409 and @entity5 buds. A total duodenopancreatectomy, including total splenectomy and gastrectomy, was performed, along with two independent Roux-en-Y anastomoses (one esojejunal and one hepaticojejunal). The @entity5 also had a wide opening in the stomach. The @entity1 's postoperative course was marked by partial @entity715 of the portal vein, which was treated medically. Histopathological examination provided evidence of pancreatic @entity3981 . The diagnosis of @entity3981 should be considered in the presence of cutaneous lesions, which were absent in the case of our @entity1 , and colonoscopy is also highly desirable because of the various forms associated with @entity1412 . The prognosis, which includes a 5-year survival rate of 45%, in the population with an R0 resection is better than that for ductular @entity420 , thus prompting the more aggressive management of this type of @entity5 .
