Intrahepatic biliary mucinous XXXX : clinicoradiological characteristics and surgical results.

@entity1 @entity5409 @entity66 @entity96 @entity5 @entity490 @entity99 @entity9296 @entity1125 @entity7157
BACKGROUND: Intrahepatic biliary mucinous @entity5 are rare @entity99 and account for less than 5% of @entity5409 . Accurate preoperative diagnosis is difficult and the outcome differs among various treatment modalities.The aim of this study is to investigate the clinico-radiological characteristics of @entity1125 and to establish eligible diagnostic and treatment suggestions. METHODS: Nineteen @entity1 with intrahepatic @entity9296 and two @entity1 with @entity7157 were retrospectively reviewed. Their clinico-radiological variables and survival outcome were analyzed. RESULTS: Of the 19 @entity1 with @entity9296 , 16 (84.2  %) were female. 11 (57.9  %) @entity1 had symptoms before operation with the most common presenting symptom being @entity490 . Among the @entity1 with available data, serum and cystic fluid CA 19-9 levels were invariably elevated and the CA 19-9 level in the cystic fluid was significantly higher than that in the serum. Loculations (84.2  %) and septations (63.2  %) were the most common radiologic findings. For treatment, 11 (57.9  %) @entity1 received radical resection by either enucleation or hepatic resection, while the remaining 8 (42.1  %) @entity1 underwent only fenestration of @entity96 . Radical resection provided a significantly better clinical outcome than fenestration in terms of @entity5 recurrence (p   =   0.018). The only two male @entity1 with @entity7157 received radical hepatic resection and achieved a @entity66 .5  months and 33  months, respectively. CONCLUSION: Intrahepatic biliary mucinous @entity5 are rare and preoperative diagnosis is difficult. Internal septations and loculations on radiologic examinations should raise some suspicion of this diagnosis. Complete @entity5 excision is the standard treatment that may provide @entity1 with better long term results after the operation.
