Paroxysmal kinesigenic XXXX .

@entity1 @entity22813 @entity3520 @entity909 @entity5516 @entity3174 @entity8684 @entity717
A healthy intelligent 13.5-year-old @entity1 is reported who presented with paroxysmal kinesigenic @entity8684 . He had had unilateral tonic spasms for 2 months. In a stressful situation, especially after a period of immobility, a @entity717 provoked a @entity3520 -choreoathetoic posturing of the left arm and leg. Attacks were brought on, for instance, by standing up quickly from a sitting position. They lasted only 5-10 s, without @entity909 and occurred up to ten times daily. Between the attacks there were no abnormalities. Family history was non-contributory. Neurological examination and laboratory findings, including repeated EEGs, were all negative. The @entity1 responded very well to @entity3174 treatment and has now been completely free of @entity3520 attacks for a period of 9 months. The importance of early recognition of this syndrome and the differential diagnosis with @entity5516 and other forms of @entity22813 is discussed.
