XXXX . A 10-year review.

@entity1 @entity101 @entity409 @entity1578 @entity281 @entity2876 @entity1575 @entity204 @entity255
The surgical results in 39 @entity1 operated on for @entity2876 at Red Cross War Memorial @entity1 's Hospital between January 1975 and January 1985 are reported. The mean age at operation was 12.8 weeks (range 6 weeks-6 months). In the first 4 years no @entity1 had sustained bile drainage after operation. Since 1979 16 of 32 @entity1 (50%) have had significant bile drainage. Of these, 8 are alive and have been followed up from 6 months to 6 years after operation. Five are jaundice-free and well. The other 3 are mildly jaundiced, have evidence of ongoing @entity409 , and have a poor prognosis. The @entity204 were due to progressive @entity409 with @entity1578 , portal @entity101 , and intercurrent @entity281 . @entity255 after 'successful' porto-enterostomy was the main cause of poor prognosis and can be related to the age at referral and the presence of @entity1575 at the time of surgery; thus bile drainage does not necessarily equate with cure. Early referral of @entity1 with conjugated hyperbilirubinaemia to a major centre is of paramount importance if we are to improve the prognosis.
