Clinicopathological features of XXXX .

@entity1 @entity24428 @entity66 @entity882 @entity548 @entity5 @entity1133 @entity16970 @entity2279 @entity881 @entity9493 @entity1365 @entity2280 @entity288
@entity24428 ( @entity24428 ), an intermediate @entity5 of endothelial origin in childhood, is often associated with @entity16970 ( @entity16970 ). In this study, 22 cases of @entity24428 were immunochemically studied for @entity2279 , @entity2280 , @entity9493 , smooth muscle actin (SMA), D240, @entity1365 and Ki67. The @entity1 (15 males and 7 females) ranged in age from 13 days to 7 years (median, 2 mo). Lesion developed on the extremities/joint (12 cases), chest/abdominal wall (6 cases), head/neck (4 cases), and presented both superficial and deep soft tissue. The superficial change was commonly enlarging cutaneous lesion with ill-defiined red to purple indurated plaque. 15 of the 22 cases (68%) developed @entity16970 , with consumptive @entity882 or @entity548 complications. @entity5 consisted of infiltrating nodules of fascicles of spindleshaped endothelial cells and slitlike vascular channels with @entity5 margins. On immunohistochemistry (IHC), endothelial cells were diffusely positive for @entity2280 , @entity2279 and @entity9493 but negative for @entity1365 , and the peripheral area of proliferative capillaries were markedly positive for D240. Adjuvant medical therapy and sclerotherapy were prepared for the @entity5 and the associated @entity16970 , and then all @entity1 were treated by complete surgical excision. Follow-up information was available in 22 @entity1 (8 to 26 months, mean 15 mo), and indicated that 1 died of @entity881 and 21 were alive without @entity66 . In conclusion, our results suggest that @entity24428 can occur in the embryonic period, and @entity1 with @entity16970 often have earlier onset time and larger lesional size. @entity24428 @entity1 given with adjuvant @entity288 and @entity1133 injection and complete resection rarely relapse.
