XXXX : Periodontists' Perspective.

@entity1 @entity32 @entity27221 @entity604 @entity26903 @entity751 @entity2521
@entity751 is a very rare disorder of autosomal recessive inheritance distinguished by @entity27221 and early onset of @entity2521 affecting the dentition. Genetic studies have identified a mutation in the major gene locus of chromosome 11q14 with loss of function. @entity26903 gene is to be responsible for @entity751 . The present case report describes a 13-year-old female, who visited the Department of Periodontology with the chief compliant of bleeding gums and loose teeth. She presented with the signs and symptoms of @entity751 . The @entity1 had premature shedding of her deciduous dentition. On clinical examination, extraorally, the @entity1 presented with persistent thickening, flaking, and scaling of the skin of palms and soles. Her intraoral examination revealed @entity32 , abscess formation, and periodontal pockets. Her intraoral radiographs showed @entity604 involving the central incisors and molars. The @entity1 underwent periodontal therapy and is under maintenance.
