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@entity808 @entity1 @entity1263 @entity5 @entity1350 @entity1352 @entity1653 @entity1583 @entity361 @entity4847
@entity5 of peripheral nerve are largely neuroectodermal in nature and derived from 2 elements of nerve, Schwann or perineurial cells. In contrast, @entity361 affecting peripheral nerve are rare and are derived mainly from epineurial connective tissue. The spectrum of the latter is broad and includes @entity1350 , @entity1583 , and even @entity1653 . Of @entity1263 , the vast majority are primary @entity1263 . Malignancies of mesenchymal type are much less common. To date, only 12 cases of @entity1352 of nerve have been described. Whereas in the past, parallels were drawn between @entity1352 and @entity5 , an uncommon form of @entity808 , molecular genetics have since clarified the distinction. Herein, we report 10 additional examples of molecularly confirmed @entity1352 , all arising within minor or major nerves. Affecting 7 female and 3 male @entity1 , 4 @entity5 occurred in pediatric @entity1 . Clinically and radiologically, most lesions were initially thought to be @entity4847 . On reinterpretation of imaging, they were considered indeterminate in nature with some features suspicious for @entity5 . @entity1352 of nerve, albeit rare, seems to behave in a manner similar to its more common, soft tissue counterpart. Those affecting nerve have a variable prognosis. Definitive recommendations regarding surgery and adjuvant therapies await additional reports and long-term follow-up. The literature is reviewed and a meta-analysis is performed with respect to clinicopathologic features versus outcome.
