Clinical experience of XXXX in Taiwan with emphasis on the treatment and survival.

@entity1725 @entity1 @entity5
BACKGROUND/AIMS: @entity1725 is a rare @entity5 with intra-abdominal gelatinous, jelly-like fluid accumulation. To assess the clinical characteristics, treatment modalities, and predictors of survival of @entity1725 in Chinese @entity1 , we conducted this study. METHODOLOGY: Over a 27-year period, 15 @entity1 with the diagnosis of @entity1725 were enrolled. Their demographic, clinical, treatment and survival data were collected. RESULTS: Seven @entity1 were female and eight were male. The median age at diagnosis was 48 years old for 7 females and 66 years old for 8 males. Exploratory laparotomy and debulking surgery were performed for 11 @entity1 (73%); 6 of these 11 @entity1 received adjuvant chemotherapy. Among 4 @entity1 without surgical treatment, 1 received chemotherapy and 3 had supportive treatment only. The 5-year survival for all @entity1 and @entity1 with surgical treatment were 39% and 62%, respectively. @entity1 with surgical intervention had longer survival (median, 125 months) than those without surgical treatment (median, 8 months) (P = 0.0106). However, adjuvant chemotherapy did not further prolong the survival time (P = 0.744). CONCLUSIONS: Surgical intervention rather than adjuvant chemotherapy appears to provide a longer survival for @entity1 with @entity1725 .
