Clinical and hematological features of XXXX in Rio de Janeiro, Brazil.

@entity1 @entity13654 @entity648 @entity381 @entity158 @entity382
1. Thirty-two @entity1 with hemoglobin SC (Hb SC) disease from Rio de Janeiro, Brazil, are described. Mean @entity1 age at the time of study was 20 years, and average age at onset nine years. 2. The main complaint at presentation was @entity158 . Symptoms involved @entity158 in 72% of the @entity1 , while 59% presented @entity382 and 50% @entity381 . Mean hemoglobin level was 10.6 g/dl, erythrocyte count, 3.9 X 10(6)/mm3, and serum @entity648 , 1.4 g/dl. Reticulocytes and Hb F were 3.0% and 2.2%, respectively. 3. The characteristics of @entity13654 observed in the present study did not differ significantly from those of other series studied elsewhere. This relative homogeneity of data is probably related to the physiopathological mechanism that promotes sickling in this condition.
