Primary XXXX : A case presentation.

@entity1 @entity296 @entity712 @entity2783 @entity3822 @entity1582 @entity299
A young @entity1 with primary @entity299 presented clinically as a case of 'restrictive' @entity296 with an initial diagnosis of @entity3822 , probably of tuberculous origin. Cardiac catheterization showed features compatible with @entity296 or @entity3822 but pericardial biopsy was negative. Percutaneous right ventricular endomyocardial biopsies established amyloid infiltration of the myocardium, but rectal, tongue and liver biopsies were all negative for @entity2783 . Bence-Jones protein was absent from the urine. Serum electrophoresis, immunophoresis, and bone marrow examination all failed to detect possible multiple @entity1582 as a cause of secondary @entity2783 . Respiratory function tests showed a restrictive picture, probably secondary to chronic @entity712 . Thus, this case is the second example of primary @entity299 in the world literature which has been dianosed by right ventricular endomyocardial biopsy. Phonocardiographic features of early aortic valve closure are reported for the first time in @entity296 . Since tuberculous @entity3822 is an important cause of @entity299 in this country, with effective therapy, the authors stress more frequent use of endomyocardial biopsy as a safe diagnostic tool to exclude other similar disease states. The @entity1 was offered the possibility of a cardiac transplantation in view of the localized nature of his disease, but refused. He now continues to respond unsatisfactorily to antifailure therapy with, presumably, a poor prognosis.
