XXXX . Surgical series of 14 cases with review of the literature.

@entity1 @entity129 @entity808 @entity1276 @entity1036 @entity5 @entity4254 @entity158 @entity204
A consecutive series of 14 @entity1 with @entity808 managed surgically at the Neurological Institute of New York since 1970 is reported. Nine @entity1 and five @entity1 (mean age 40 years) were diagnosed following a mean symptom duration of 33 months. Abnormalities of trigeminal nerve function were present in 11 @entity1 on admission examination. @entity158 was a prominent feature in eight @entity1 . Two @entity1 , both with @entity808 arising from the trigeminal root, presented initially with typical @entity4254 . Additional @entity129 or cerebellar or pyramidal tract signs were noted in eight @entity1 . The surgical approach to these @entity5 depends on their anatomical location. Four @entity1 had @entity5 confined to the middle fossa, three @entity1 had @entity5 limited to the posterior fossa, and seven @entity1 had both supratentorial and infratentorial components of their @entity5 . Twenty operative procedures were performed on these @entity1 , resulting in complete extirpation in six @entity1 , nearly complete removal in seven @entity1 , and partial removal in one @entity1 . Adherence of the @entity5 to the lateral wall of the cavernous sinus or the brain stem precluded total removal. There was one @entity204 . In the immediate postoperative period, @entity129 controlling the extraocular muscles were common. In general, these deficits were transient; however, some permanent loss of trigeminal nerve function occurred in nine @entity1 . Two @entity1 required tarsorrhaphy for @entity1036 , and two @entity1 underwent cerebrospinal fluid (CSF) shunting procedures for @entity1276 or for a persistent CSF leak. The follow-up period ranged from 4 to 177 months (mean 47 months). The clinical features, anatomical considerations, and surgical approach to these rare @entity5 are discussed. A clinical review of 106 additional cases of @entity808 , reported in the English literature since 1935, is also presented.
