[ @entity7611 . A type with vascular @entity715 and XXXX ].

@entity1 @entity1501 @entity7611 @entity2764 @entity2245 @entity3959 @entity5630 @entity2186 @entity1853 @entity3459 @entity7727 @entity715
In @entity7611 , @entity715 is frequent (50% of the cases). The authors report a case of @entity3959 -synthetase deficiency-induced @entity7611 associated with @entity715 of a common iliac vein. This @entity1 presented with a @entity3459 which was related to severe @entity5630 and which was corrected by treatment. @entity7611 was @entity2764 independent as witnessed by the fact that Brand's reaction remained positive with @entity2245 therapy and @entity3959 . @entity3959 -synthetase activity measured in cultured fibroblasts increased only slightly with @entity2764 therapy. Treatment ( @entity7727 , @entity1501 , @entity2186 ) induced the disappearance of plasma @entity1853 . Clinically, the @entity1 whose treatment came late in the course of her disease, was only slightly improved. Hypotheses about etiopathogenic mechanisms of this disease are discussed. Difficulties of treatment and diet are reviewed. The relative inefficacy of therapy, even in case with early treatment, makes antenatal diagnosis preferable to neonatal diagnosis.
