[Right ventricular dysplasia: clinical characteristics of five XXXX ].

@entity1 @entity1165 @entity5988 @entity714 @entity1353 @entity4 @entity1283 @entity997 @entity1001 @entity382 @entity955 @entity4266
The purpose of this study was to elucidate the clinical features of @entity4266 , a recently described clinical entity characterized by RV myopathic changes and @entity1165 of @entity714 morphology. Five cases were reported, in which the diagnosis was established according to the criteria of Marcus. Case 1, a 33-year-old @entity1 , was referred to us for evaluation of his paroxysmal @entity1165 of five years duration. Case 2, a 38-year-old @entity1 , was admitted because of shock caused by @entity1165 . In both cases, the QRS configurations during @entity1165 were those of the @entity714 pattern, and electrocardiograms during sinus rhythm showed T wave inversions in the right precordial leads and late ventricular potentials. Two-dimensional echocardiography, radionuclide angiography and contrast angiography disclosed @entity1001 with normal left ventricular (LV) function. The biopsied myocardium from the right and left ventricles in Case 2 revealed myocytolysis, a paucity of myofibrils and proliferation of collagen fibers. Case 3, a 73-year-old @entity1 began to experience exertional @entity1353 since 16 years of age. Her treatment consisted of bed rest, diuretics and digitalis. In December 1983, her New York Heart Association functional class was III, and physical examinations disclosed a Levine III/VI systolic murmur suggestive of @entity997 , jugular vein dilatation, @entity382 , and pretibial @entity4 . Electrocardiogram showed @entity955 , incomplete @entity714 and T wave inversions in the precordial leads. Chest radiograph revealed marked @entity1283 (cardiothoracic ratio of 92%). Echocardiography, radionuclide angiography and contrast angiography revealed marked @entity1001 , depressed ejection fraction (RV end-diastolic volume index of 342 ml/m2, and RV ejection fraction of 28%). Case 4, a 20-year-old @entity1 , was admitted with a chief complaint of palpitation. Case 5, a 19-year-old @entity1 , was referred to us for the evaluation of asymptomatic @entity1283 , and his cardiothoracic ratio was 54%. A 12-lead electrocardiogram showed @entity714 and T wave inversions in the right precordial leads. Ambulatory electrocardiography revealed frequent premature ventricular complexes of the @entity714 pattern. Echocardiography, radionuclide angiography, and contrast angiography disclosed @entity1001 in both cases, and mild @entity5988 and dysfunction (LV end-diastolic volume index of 149 ml/m2, LV ejection fraction of 48%) in Case 4.(ABSTRACT TRUNCATED AT 400 WORDS)
