Surgical Treatment of Primary XXXX : Review of a Single-Institution Experience.

@entity1 @entity242 @entity5 @entity5426 @entity4617 @entity299
BACKGROUND: Primary @entity299 are rare, aggressive, and usually lethal. Surgical management protocols are not defined because of the lack of extensive experience in treating these @entity1 . In this study, we reviewed our outcomes with primary @entity299 , and we make recommendations regarding management. METHODS: Review of the Houston Methodist Hospital @entity4617 database from 1990 to 2015 (25 years) yielded 131 primary cardiac evaluations of possible @entity299 . From these we identified 95 @entity1 who underwent surgical excision. A computer search of @entity299 yielded 131 @entity5 that were coded as primary @entity299 or possible primary @entity299 . Retrospective data collection and clinical outcomes were evaluated for all 95 @entity1 . Medical records and follow-up material were requested for all @entity1 through clinic visits and contacting the physician of the @entity1 , the hospital record department, and the @entity4617 board after previous approval. The procedures were performed using an institutional review board-approved @entity4617 protocol, and the @entity1 gave full consent. RESULTS: All 95 @entity1 were diagnosed as having primary @entity299 by histologic appearance. Age ranged from 15 to 84 years at the time of presentation (mean, 44 years). Male @entity1 made up 57% of the sample. The most common site for the @entity299 was the right atrium (37 @entity1 ) followed by the left atrium (31 @entity1 ). Postoperative 1-year mortality was 35% (33 @entity1 ). The most common @entity5 histologic type was @entity5426 (40%) followed by @entity242 (11%). CONCLUSIONS: Primary @entity299 is a rare but lethal disease. Surgical intervention is associated with acceptable surgical mortality in this high-risk group of @entity1 .
