Heterotaxy and XXXX : 20 years experience at a UK regional paediatric surgery centre.

@entity1 @entity717 @entity981 @entity712 @entity3313 @entity10094 @entity299 @entity4032
BACKGROUND: The association of @entity4032 with @entity717 is well described. However debate exists with regard optimal management notably should 'asymptomatic' @entity717 undergo operation? The present study therefore sought to determine: (1) the risk(s) of @entity3313 in @entity1 diagnosed with @entity4032 and (2) define morbidity associated with operation for ' @entity10094 in a fragile @entity1 cohort with co-existent @entity299 . METHODS: Medical case record reviews of @entity981 @entity1 born during January 1993-December 2013 and attending a UK paediatric centre were analyzed. RESULTS: Of a total of 92 @entity1 , 16 (17.4%) cases underwent foregut imaging studies. Three examinations were performed in 'symptomatic' @entity1 . Twelve studies reported 'abnormal anatomy' with only five @entity1 undergoing surgical correction. No complication(s) were recorded after Ladd's operation to correct defects. A single fatality occurred within 30 days postoperatively from @entity712 . In 87 @entity1 in whom Ladd's operation was not undertaken, no single @entity1 developed @entity3313 (median length of follow-up 27.2 months, total 446.1 @entity1 years). CONCLUSION: This study strongly supports a 'watchful waiting' policy for @entity4032 @entity1 . Many @entity1 who ultimately die from @entity299 may avoid unnecessary abdominal surgery.
