Occurrence of @entity449 in 5 cases of XXXX .

@entity1 @entity449 @entity17454 @entity439 @entity158
@entity449 are a rare condition in @entity1 . Here we report the occurrence of @entity449 in 5 @entity1 with @entity17454 ( @entity17454 ). Three @entity1 had a @entity17454 score of 4, and 2 @entity1 had a @entity17454 score of 5, but autoimmunity was only present in 1 @entity1 . Discovery was fortuitous in 4 cases after chest radiography or thoracic or abdominal computed tomography, which was performed to investigate unrelated symptoms; in 1 @entity1 , @entity158 was an alerting sign. Age at diagnosis was 10 to 16 years. @entity439 were confined to the thoracic aorta in 4 cases and to the abdominal aorta in 1 case and were from 2 to 6 cm in size. Aortic surgery was successfully performed on the single symptomatic @entity1 . Two other @entity1 are alive: there has been a low progression of the @entity439 15 years after hematopoietic stem cell transplantation in 1 @entity1 and no evidence of progression after 12 years of follow-up without hematopoietic stem cell transplantation in the second @entity1 . Two @entity1 died 2 and 4 years after diagnosis from unrelated complications. A systematic retrospective search of 33 other @entity1 with @entity17454 for whom imaging material was available did not reveal the presence of @entity449 . This unusual frequency of @entity449 found in @entity1 with @entity17454 (5 of 38) indicates that @entity439 can be an underdiagnosed complication of @entity17454 . It is presently unclear whether it is caused by an infectious and/or autoimmune/inflammatory process. Therefore, we suggest that @entity439 of large vessels should be systematically searched for in @entity1 with @entity17454 .
