XXXX : evaluation of reported cases.

@entity1 @entity5 @entity1358 @entity23845 @entity158
PURPOSE: We present the cases of 4 @entity1 with @entity1358 and a contrasting case of a @entity1 with a @entity23845 from Massachusetts General Hospital. Differential diagnosis, distinguishing characteristics, and data from 32 cases in the literature are also reported. Because this rare @entity5 behaves aggressively with both regional and distant spread, a better understanding of its biologic behavior is imperative. @entity1 AND METHODS: The 4 @entity1 with @entity1358 were @entity1 and had an average age of 65 years (range, 40 to 77 years). Three @entity5 were in the posterior mandible and 1 was in the maxilla. Three @entity1 complained of @entity158 ; bony expansion and tooth mobility were noted in isolated cases. A comparison is made with other reported cases, and factors associated with recurrence and survival are presented. RESULTS: All @entity1 were treated with resection, and 1 @entity1 received postoperative radiotherapy. Two @entity1 with positive surgical margins underwent further resection. All @entity1 have been followed an average of 2 years (range, 0.5 to 4 years) and presently have no evident disease. CONCLUSIONS: Recognition of this @entity5 and differentiating it from other clear cell neoplasms is critical in developing an appropriate treatment plan. Management should include wide en bloc resection and long-term follow-up.
