[Natural history of XXXX elucidated by pulmonary hemodynamics].

@entity1 @entity712 @entity120 @entity519 @entity67
The present study was undertaken to clarify the natural history of @entity120 ( @entity120 ) from a hemodynamic point of view. The subjects consisted of 83 @entity1 (18 @entity1 and 65 @entity1 ), whose ages ranged from 14 to 69 years and averaged 33 years. They were contacted through a nationwide survey. All @entity1 underwent right-sided cardiac catheterization; cardiac output was measured in 52 @entity1 and pulmonary capillary wedge pressure, in 40 @entity1 . The following results were obtained. 1. The @entity1 who died within three months of their cardiac catheterization were in severe @entity67 as shown by their elevated right atrial pressures and decreased cardiac indices. 2. The @entity1 who died suddenly within two years of their cardiac catheterization had the same degree of @entity67 . The only difference was severe @entity519 in the @entity1 with @entity712 (54 +/- 21 vs 66 +/- 4 mmHg, p less than 0.05). 3. The @entity1 who survived more than two years had normal right ventricular function. 4. Among the hemodynamic variables used to estimate prognosis; namely, pulmonary artery diastolic pressure, pulmonary capillary wedge pressure, cardiac index, pulmonary vascular resistance and pulmonary to systemic vascular resistance ratio, the cardiac index was the best predictor of prognosis.
