[A case of XXXX of the thoraco-abdominal aorta associated with Beh  et's disease].

@entity1 @entity439 @entity158 @entity2849 @entity1756
A 41-year-old male with incomplete type of Beh  et's disease was operated on because of @entity1756 of the thoraco-abdominal aorta. A saccular @entity2849 developed by rupture of the aortic wall involved the left postero-lateral portion of the supra-renal abdominal aorta. The defect in the @entity439 was closed using Dacron patch. The post-operative course was uneventful. However, seven months after discharge, the @entity1 developed severe back @entity158 at midnight, and was referred to our institution. On physical examination, a pulsatile mass was found in the right epigastric area. CT and DSA showed saccular @entity2849 at the patch anastomotic site. Extra-anatomic long bypass grafting was performed from the ascending aorta to the infra-renal abdominal aorta. The abdominal aorta was occluded just below the diaphragm and the supra-renal portion of the aorta. Reconstruction of coeliac artery and superior mesenteric artery was made using branch grafts attached to the long graft. Surgical treatment of the complicated Beh  et's disease should include extra-anatomic bypass, especially in the re-operative cases of @entity1756 of the aorta.
