Prognostic Factors and Outcomes of Adult-Onset XXXX : A Retrospective Analysis of 34 Cases.

@entity1 @entity9472 @entity706 @entity9058 @entity5 @entity2879 @entity619 @entity1800 @entity205 @entity19865 @entity230 @entity1413 @entity204
Adult-onset @entity9058 ( @entity9058 ) has features that are distinct from that of @entity9058 in pediatric @entity1 . The clinical records at the Japanese Red Cross Kumamoto Hospital were reviewed. We retrospectively analyzed 34 @entity1 who fulfilled the diagnostic criteria of @entity9058 -2004. The median age of @entity1 was 60.0 (range 15-86). Underlying diseases were diagnosed in 17 @entity1 . They consisted of @entity706 (n=3), other @entity5 (n=3), @entity1800 (n=4), @entity1413 (n=3), @entity19865 (n=3) and drug (n=1). Underlying diseases were not diagnosed in 17 @entity1 despite examination. The treatments were @entity230 (n=18), @entity619 + @entity205 ( @entity9472 ) + @entity2879 (n=4), multidrug chemotherapy (n=2), @entity230 and @entity9472 (n=3). Eleven @entity1 died during observation. In a multivariate analysis, the significant predictor for @entity204 was age at onset (hazard ratio, 1.22; 95%CI, 1.02-1.44; P=0.027). Autopsy was performed in 4 cases, but the underlying disease remained unknown in 3 of those cases. Adult-onset @entity9058 has high diversity and various outcomes. The mechanism of adult-onset @entity9058 is not fully understood and further research is required.
