Idiopathic XXXX in childhood: a case report and review of literature.

@entity1 @entity32 @entity1635 @entity730 @entity925 @entity221 @entity2383
PURPOSE: Pediatric idiopathic @entity730 (PIIVDC) is an uncommon entity affecting the intervertebral disks and adjacent vertebral body and @entity2383 . More than 300 cases have been reported so far, but knowledge of PIIVDC is still fragmentary. The purpose of the study was to summarize the demographic and clinical characteristics of PIIVDC, and consider its treatment and natural history. METHODS: This study is a review of 65 cases identified by literature search from 1990 to 2010. RESULTS: Male-to-female ratio was 40:25. Most @entity1 (83%) were aged 5-12 years. @entity925 was the most common manifestation (71.9%), followed by sensorimotor disturbance (20.3%) and @entity221 (13.8%). Torticollis or @entity1635 were noted in 23.4% of @entity1 , and 15.4% were asymptomatic. The cervical spine was most frequently affected (64.6%), followed by the thoracic (26.2%), cervicothoracic (10.8%), lumbar (4.6%), and thoracolumbar (1.5%) spine. The C6/7 intervertebral disk was most frequently affected (35.7%), followed by C3/4 (21.4%), C2/3 (17.9%), C5/6 (14.3%), and C4/5 (10.7%). Erythrocyte sedimentation rate was the most sensitive laboratory indicator. Conservative treatment was adopted for 89.2% of @entity1 and surgery for 10.8%. Neurological outcome was excellent except for one @entity1 . CONCLUSIONS: PIIVDC appears to be a benign disorder associated with self-limiting @entity32 . The natural history of PIIVDC will only be established by further experience with long-term follow-up periods into adulthood.
