XXXX : case series with extended follow up.

@entity1 @entity1187 @entity13865 @entity453 @entity731
@entity13865 ( @entity13865 ) is @entity731 or non- @entity731 in origin. Eosinophilic infiltrate is identified in coronary artery adventitia in @entity453 . We postulate that a systemic inflammatory state causes @entity13865 in younger @entity1 who do not have significant @entity453 risk factors. We report a case series of 13 @entity1 presenting with @entity13865 from ages 26-48 with follow up from 1 month to 13 years. Most @entity1 did not have conventional risk factors for @entity453 ( @entity453 ). Approximately 50% of the @entity1 developed recurrent dissection within the first 2 weeks of an index event, but < 25% were symptomatic during follow up. All @entity1 were alive at follow up. Systemic inflammatory state was observed in 80% of @entity1 who developed early recurrent dissection. @entity13865 should be strongly suspected in younger @entity1 presenting with @entity1187 without @entity453 risk factors. Coronary dissection may recur within first 2 weeks, but @entity1 have good long-term survival without new episodes of dissection. Broad rheumatologic and connective tissue disease work-up should be considered in young females presenting with @entity13865 .
