Tetralogy of Fallot with total XXXX .

@entity1 @entity215 @entity1700 @entity713
BACKGROUND: The association of @entity215 with total @entity1700 (TAPVD) is rare. We report our experience with this condition and review the literature. METHODS: Between January 1997 and May 2008, 6 @entity1 (aged 3 months to 5 years; median weight, 10 kg) with combined @entity215 with TAPVD underwent complete primary repair at All India Institute of Medical Sciences, New Delhi, India. Their records were retrospectively reviewed. RESULTS: A correct preoperative diagnosis was available in 5 @entity1 by echocardiography and cardiac catheterization. Four @entity1 had supracardiac TAPVD, and 1 each had TAPVD to the coronary sinus and right atrium. There were no early or late deaths. Median follow-up was 37.5 months +/- 46.8 months (range, 2 to 112). All @entity1 are in New York Heart Association class I. Follow-up echocardiograms have revealed no significant abnormalities and have documented normal biventricular function and pulmonary artery pressures. One @entity1 underwent a 24-hour Holter examination at 68 months of follow-up for investigation of a new-onset 2:1 @entity713 , for which a permanent pacemaker implantation is planned. CONCLUSIONS: When diagnosed accurately, complete primary repair is possible in @entity1 with @entity215 and TAPVD and the outcomes are satisfactory with planned surgery.
