Primary XXXX in the sphenoidal bone and orbit.

@entity1 @entity9175 @entity227 @entity5 @entity16 @entity5768 @entity1503 @entity1829 @entity4585
CASE REPORT: We report a case of a primary @entity4585 in @entity1 aged 2 years and 8 months. The symptoms were progressive @entity5768 , @entity9175 , and bilateral @entity1829 . The @entity5 was partially calcified and was a round mass located in the bilateral sphenoidal bone extending into the orbit. Laboratory study did not show @entity1503 . The @entity5 was partially removed by bilateral frontotemporal craniotomy and a diagnosis of primary @entity4585 was made from the surgical specimen. Progressive @entity227 was seen and chemotherapy started on the 11th postoperative day followed by local cranium irradiation (24 Gy). The @entity1 has been in complete remission for 37 months. The visual acuity recovered partially and follow-up magnetic resonance imaging showed a significant decrease in the size of the @entity5 . DISCUSSION: Radiological diagnosis of primary intracranial @entity4585 is difficult. Surgical removal may be an option for progressive @entity16 but chemotherapy is more important for both neurological stabilization and induction of remission.
