XXXX : report of eight cases.

@entity1 @entity146 @entity303 @entity2045 @entity6694 @entity75 @entity2438 @entity2008 @entity427 @entity2055
The author reports eight cases of the @entity6694 , or @entity303 - @entity2055 - @entity2438 , in @entity1 . The cases satisfy the following criteria: Normal development in the first mos of life. Profound deterioration of the mental status over a period of several mos. @entity146 . Presence of neurological signs such as @entity2055 , @entity2045 and @entity427 . Normal head circumference at birth, but subsequent subnormal growth. EEG abnormalities. Slow progression of the disease after the period of rapid deterioration. The constellation of the signs and symptoms, and the occurrence only in @entity1 , make this clinical picture quite distinct. There is no definitely known biochemical or @entity2008 . The psychological profile, though homogeneous in all the @entity1 , is not pathognomonic, and a very similar behavioral pattern can be observed in other @entity75 .
