XXXX : clinical course and prognosis with a special view to long-term functional results.

@entity1 @entity322 @entity3313 @entity548 @entity1494 @entity5 @entity73 @entity189 @entity600 @entity44
From 1976 to 1995, 23 @entity1 , 4 @entity1 and 19 @entity1 , were treated at our department for @entity44 ( @entity44 ). Their records were analyzed retrospectively, considering age at operation, histopathology, recurrences, and long-term evolution. One died on the 1st day of life following @entity5 rupture with @entity548 without surgical intervention. All others were operated upon at a mean age of 4.2 days for those 19 (= 82%) who were diagnosed in the neonatal period and whose histology proved benign. In the remaining 3 @entity1 , in whom @entity5 manifestation did not occur before 11 months, 13 months, and 10 years of age, respectively, histopathologic evaluation revealed 2 @entity189 and 1 yolk-sac @entity5 , and all 3 recurred. Overall, 5 @entity1 died, the 1 mentioned above, 1 due to @entity3313 after laparotomy, and 1 from multiple associated @entity600 . Two deaths were related to @entity5 , whereby only 1 was a malignant @entity44 diagnosed at the original operation. Eight @entity1 had recurrences, 2 were benign and 6 malignant, with 3 of the latter having been graded benign on histology of the @entity5 . Of the 18 surviving @entity1 , 17 (93.5%) returned for clinical review following a standardized protocol. The average interval from the primary surgery was 12.3 years (range 3.5-22 years). Four had @entity5 with a recurrence-free period of from 9 to 14 years; 5 (29.4%) had @entity73 . One @entity1 with a patulous anus presented with fecal soiling. Two reported nocturnal enuresis, 1 associated with perineal anesthesia. One had a @entity1494 with overflow voiding and bilateral third-degree vesicoureteral reflux. Second-degree reflux was found in the last @entity1 . We conclude that follow-up after surgery for @entity44 should not only search for @entity5 recurrence but include the diagnosis and treatment of possible secondary urinary and/or fecal @entity322 .
