Inflammatory pseudotumor of eyelid: a probable IgG4-related @entity66 clinically mimicking eyelid XXXX .

@entity1 @entity66 @entity706 @entity5 @entity75 @entity262 @entity1463 @entity1892 @entity134 @entity17390 @entity617
BACKGROUND: Ocular adnexal IgG4-related @entity66 (IgG4-SD) has been categorized as a novel disease entity. It is characterized by @entity1463 and an infiltration of mass-forming lymphoplasmic cells containing many IgG4-positive plasma cells. Although ocular adnexal tissue involvement has been increasingly reported, a focal nodular sub-brow mass is not typical in an IgG4-SD presentation. We report a rare case of probable ocular adnexal IgG4-SD that clinically mimicked eyelid @entity17390 . CASE PRESENTATION: A 42-year-old @entity1 presented with a nodular mass in her left sub-brow area. The initial clinical impression of her lesion was eyelid @entity17390 . However, the final pathologic diagnosis was IgG4-SD, but extranodal marginal zone @entity1892 could not be excluded. The @entity1 underwent testing to determine @entity5 malignancy and systemic IgG4-SD involvement. Laboratory testing showed normal IgG and IgG4 serum levels and imaging revealed no remarkable findings. Oral @entity617 was administered and slowly tapered to manage the possible @entity75 and to prevent disease recurrence. Two years after initiating therapy, there was no evidence of relapse. The @entity1 is under close surveillance for signs of recurrence, systemic involvement, and potential malignant transformation. CONCLUSIONS: We found an unusual case of probable ocular adnexal IgG4-SD, which presented as a unilateral restricted mass involving the sub-brow area. Although the mass was surgically removed, systemic @entity134 treatment and long-term surveillance were initiated due to the possibility of recurrence, the potential association with @entity262 , and the potential development of extranodal mucosa-associated lymphoid tissue (MALT) @entity706 .
