XXXX in the paediatric population: presentation and treatment of head and neck manifestations.

@entity1 @entity3329 @entity66 @entity1910 @entity2522 @entity1222 @entity79 @entity12088 @entity2267
@entity1222 ( @entity1222 ) is a rare paediatric disease of unknown etiology affecting 1 to 5 @entity1 per 1 million each year. It is characterized by the idiopathic proliferation of Langerhans' cells. The clinical spectrum of disease is quite varied, ranging from a solitary eosinophilic granuloma to diffuse multisystem involvement. The head and neck is the most common site of involvement, occurring in approximately 60% of @entity1222 @entity1 . Head and neck manifestations are diverse and include skull and temporal @entity79 , cervical @entity3329 , and @entity1910 . Diagnosis can be difficult as these lesions mimic other common conditions seen by the otolaryngologist, including @entity12088 , acute @entity2267 , and @entity2522 . A retrospective study was carried out to study our centre's experience with @entity1222 over the last 10 years. Twenty-one @entity1 were diagnosed between January 1990 and December 1999. @entity1 's age at time of diagnosis ranged from 6 days to 14 years. Fifty-seven percent of @entity1 had localized bony lesions; the remaining 43% had @entity66 . The head and neck was also the most commonly involved site in our study, affecting 67% of our @entity1 . Presentation and diagnosis of these lesions are discussed in detail. Treatment, complications, and @entity1 outcomes will also be discussed.
