[ XXXX and risk for life].

@entity1 @entity64 @entity339 @entity944 @entity1163 @entity10804 @entity3454 @entity195 @entity943 @entity204 @entity884
Idiopathic @entity3454 , also called @entity195 , has been estimated to affect 5 p. 100 of the general population. Normally a benign disease, it becomes life-threatening in only a very small number of cases. High risk subjects could be detected by simple TM-mode echocardiography, provided this examination is of good quality and reproducible, for it shows a 5 mm or more thickening of mitral leaflets. Should this be the case, according to the Mayo Clinic authors, serious complications, such as @entity944 , @entity884 or @entity64 , would be expected to occur in 10 p. 100 of the @entity1 . @entity944 , of which only 60 cases have been published, is exceptional; it mainly concerns young subjects (mean age 40 years), predominantly @entity1 , with a family history of @entity944 , who have experienced one or several @entity1163 and present with severe per- or intercritical @entity943 . Such subjects must be regularly supervised clinically as well as by basal or ambulatory electrocardiography and, if necessary, by electrophysiological or even haemodynamic exploration. Treatment with appropriate beta-blockers or antiarrhythmic agents is often required as is, in refractory cases, implantation of an @entity10804 . @entity884 is a cause of @entity204 in 10 to 20 p. 100 of the @entity1 . It mainly threatens subjects whose @entity339 is suspected on the presence of a holo- or end-systolic murmur and confirmed by Doppler echocardiography.(ABSTRACT TRUNCATED AT 250 WORDS)
