Intraspinal XXXX --report of three paediatric cases.

@entity3570 @entity1 @entity3574 @entity292 @entity601 @entity45 @entity3558
BACKGROUND: @entity601 are rare congenital lesions of the spine and are lined with entodermal epithelium. They result from anomalous endodermal-neuroectodermal adhesion in the 3rd week of embryonic life with persistence of canal of Kovalevsky. The nature of the eventual abnormality depends on the extent to which this adhesion subsequently disappears. Persistence of the entire tract results in the extreme form of combined anterior and posterior @entity3570 with dorsal enteric @entity292 and persistence of only a part of the tract producing the isolated intraspinal cyst. The most common location is the cervico-dorsal region, and usually it lies ventral to the spinal cord. The lumbosacral location is uncommon. Associated @entity3574 , @entity45 , bowel duplication, the presence of keratin markers and @entity3558 -secreting cuboidal or columnar intestinal epithelium in their walls confirm their entodermal origin. @entity1 : We describe here three unusual cases of @entity601 in @entity1 aged 5-18 years who had already had symptoms for some time. One of these had a cyst sited predominantly in the sacral canal, another presented with a lumbar neurenteric cyst, and the third @entity1 had an intradural extramedullary thoracic lesion. Two of these @entity1 had associated anomalies, the one with lumbar cyst also having a lipomeningomyelocele and @entity3570 while the other also had deformed vertebrae. All three @entity1 underwent laminectomy and gross excision of the cysts through a posterior approach. RESULTS AND CONCLUSION: The diagnosis of @entity601 was confirmed by demonstrating @entity3558 -producing cuboidal or columnar epithelium lining the cystic cavity.
