XXXX in @entity2418 (congenital absence of hypoplasia of the thymus).

@entity1 @entity8521 @entity215 @entity1757 @entity5451 @entity509 @entity2418 @entity6127 @entity65
Partial or complete absence of the thymus ( @entity2418 , III-IV @entity2418 ) is often associated with @entity5451 or @entity509 of the parathyroid glands and, almost invariably, with @entity65 . The clinical and pathologcial findings in 10 cases proven at necropsy are presented. All @entity1 presented with cardiac symptoms and signs in the first weeks of life and, with one exception, all died of a cardiac cause. @entity65 were found in all 10 cases. Four had, in association with a @entity1757 of the infundibular type, an interrupted @entity8521 , which was left-sided in two and right-sided in two other cases. Four @entity1 had truncus arteriosus type I, in two of them associated with a right-sided @entity8521 . Two @entity1 with @entity215 had a right-sided @entity8521 . Only two of the 10 had a normally developed left @entity8521 . Aberrant subclavian arteries were found in five cases. From our observations and a survey of the previously published @entity1 it appears that 90 per cent of the necropsy-proven cases of @entity2418 have @entity65 and that 95 per cent of these malformations can be classified as @entity6127 , truncus ateriosus, or @entity215 .
