Incidence of @entity572 Associated With XXXX .

@entity1 @entity154 @entity1494 @entity8482 @entity600 @entity9960 @entity7891 @entity572 @entity3029
BACKGROUND: @entity1494 is a rare @entity154 seen in 2.15 @entity1 out of every 100,000 live births, with the most severe variant, @entity7891 ( @entity7891 ), only occurring in 1 in 200,000. @entity572 ( @entity572 ) describes a spectrum of disease ranging from mild hip instability to @entity3029 . Underlying @entity600 , such as @entity9960 and @entity8482 , are often associated with the most severe variant of @entity572 , teratologic @entity572 . The varying degrees of severity in @entity572 have been encountered in classic @entity1494 (CBE) @entity1 , but the exact incidence is unknown. We sought to determine the incidence of @entity572 in CBE and @entity7891 @entity1 . METHODS: We performed a retrospective review of all @entity1 with CBE or @entity7891 presenting to a single pediatric center between 1994 and 2014. Each chart was reviewed for correct diagnosis of CBE or @entity7891 , @entity1 age and demographics, associated medical conditions, pertinent surgeries performed, and the age at operation. @entity1 imaging was reviewed to determine whether bilateral hip imaging was available. RESULTS: In a 20-year retrospective review, we identified 66 @entity1 who were diagnosed with either CBE or @entity7891 and had available hip imaging (38 males and 28 females). Of these, 11 @entity1 were found to have radiographic evidence of @entity572 , for an incidence of 16.7% (11/66). Five of these @entity1 had @entity7891 , whereas 6 presented with CBE. The first radiographic evidence of @entity572 was noted at a mean age of 5.75 years (range, birth to 22 y). CONCLUSIONS: We advocate the use of routine hip screening ultrasound in all @entity1 born with either CBE or @entity7891 . Early identification of @entity572 in these @entity1 may allow additional treatment options to coincide with frequently used osteotomy and orthopaedic interventions. LEVEL OF EVIDENCE: Level III-retrospective study.
