Primary XXXX : case report and review of the literature.

@entity1 @entity1087 @entity167 @entity4 @entity409 @entity1109 @entity1003 @entity425 @entity828 @entity177 @entity3043 @entity1578 @entity1892 @entity490 @entity1893 @entity10 @entity99 @entity221
A 31-yr-old @entity1 presented with a 1-wk history of @entity221 , chills, @entity425 , @entity10 , and a significant 20-lb weight loss over the preceding 2 months. His past medical history was relevant for @entity409 during childhood. Two days before admission, the @entity1 noticed @entity1087 . He denied @entity490 or other @entity1109 , and there was no history of @entity167 intake, medications, or illicit drugs. His physical examination revealed generalized @entity1087 , @entity828 , and bilateral leg @entity4 . Neurologically, the @entity1 was agitated, with periods of disorientation, and he had bilateral flapping. His blood tests revealed @entity3043 , @entity177 , @entity1578 , and @entity1003 . Because the @entity1 had a @entity221 , @entity828 , and @entity3043 , a further workup also included a bone marrow and liver biopsy. No conclusive diagnosis could be made from the above tests, and the @entity1 died 5 days after admission. Postmortem evaluation, including flow cytometry and gene rearrangement in the tissue obtained from the liver, revealed @entity1892 . This case illustrates an unusual presentation of @entity1893 . Current information regarding this entity is scant, mainly owing to its rarity. We present a review of the literature, including the incidence, presentation, treatment, and prognosis of primary @entity99 .
