Mixed @entity444 and dysgenetic XXXX .

@entity1 @entity4998 @entity2650 @entity5 @entity31936 @entity444
Mixed @entity444 and dysgenetic @entity31936 are 2 forms of @entity31936 that present with absent m  llerian regression and @entity4998 . We present a retrospective analysis of 10 @entity1 with the diagnosis of either mixed @entity444 or dysgenetic @entity31936 encountered during a 16-year period at our institution. We assigned a female gender to 4 @entity1 and a male gender to 3. Three @entity1 were assigned a male gender before referral (2 for whom we would have preferred female assignment). All intra-abdominal gonads were removed except in 2 @entity1 assigned a male gender who underwent bilateral orchiopexy. @entity1 underwent @entity2650 repair or feminizing genitoplasty depending upon the gender assigned. Although female gender assignment is usually preferred, male assignment is a justifiable alternative in instances of extreme virilization and a descended testis. However, in these male assigned @entity1 , consideration must be given to the role of periodic testicular biopsies. In light of @entity5 potential, all intra-abdominal gonads should be removed. When necessary, appropriate surgical genitoplasty should be performed at an early @entity1 age.
