[ XXXX of the temporal bone. Case report and literature review].

@entity1712 @entity1 @entity22964 @entity1222 @entity2879 @entity2281 @entity4896 @entity5713
BACKGROUND: @entity1712 , Hand-Sch  ller-Christian disease an @entity1222 are characterised by ideopathic proliferation of histiocytes producing focal or systemic manifestations. Definitive diagnosis of @entity22964 is made by histopathology including immunohistochemical detection of @entity2281 and @entity4896 antigens. In general these diseases are summarised under the term @entity1222 ( @entity1222 ). The localised form of @entity1222 , in which the disease is limited to bones, lymphatic nodes or the lung, is commonly referred to as @entity1712 . Surgical excision, radiotherapy and chemotherapy, either alone or in combination, are the main treatment options. CASE REPORT: We present the case of a nine-year old @entity1 with an extended @entity1712 of left temporal bone. The @entity1 was submitted to a chemotherapeutic protocol with glucocorticoids, @entity5713 and @entity2879 . Until today a successful treatment and a complete remission for one year can be reported. CONCLUSIONS: Unifocal @entity1712 is usually treated by local excision and low-dose irradiation. However treatment with the chemotherapeutic protocol offered an excellent alternative avoiding extensive surgical destruction of the temporal bone in this case.
