[A family of von @entity1264 complicated by mononeuritis multiplex, bilateral acoustic neurinomas, and falx and XXXX ].

@entity5513 @entity1313 @entity5 @entity1264 @entity10 @entity735 @entity1653 @entity194 @entity1736 @entity393 @entity912 @entity29804 @entity1848
A family of @entity1264 complicated by multiple diverse primary @entity1313 was reported. Case 1. The proband, born in 1923, was admitted to the Nagasaki University Hospital on @entity29804 , 1974, for evaluation of @entity10 and @entity393 . Neurological examination disclosed: decreased visual acuity on the right: bilateral choked discs; anisocoria, right pupil wider than left; right @entity1736 ; artificially fixed @entity735 ; right facial @entity912 ; markedly impaired hearing with negative vestibular responses to caloric test; paralysis of the right soft palate and vocal cord; @entity194 of the right side of the tongue; right @entity1848 with positive Froment's sign; left drop foot; loss of deep reflexes on the left arm and legs; positive Babinski on the right. Nerve conduction studies revealed failure to evoke muscle action potential in response to electric nerve stimulation on the left ulnar and right superficial peroneal nerves. Needle electromyography showed no motor unit potentials in the left first dorsal interosseus and right anterior tibial muscles. Sensory nerve action potentials could not be evoked on any nerves tested. X-ray films showed enlargement of the internal auditory passages, falx @entity5 on brain scan and carotid angiography, and @entity5 on myelography. At craniotomy, a 7 X 5.5 X 4 cm falx @entity1653 was removed. At suboccipital craniotomy performed five weeks later, right @entity5513 measuring 1.5 cm in diameter was removed. Case 2. This relative, born in 1945, was the son of the proband. A @entity1653 at C 7-T 1 was removed in 1957. However, he could not walk after operation and died of pneumonia two years later.(ABSTRACT TRUNCATED AT 250 WORDS)
