XXXX involving the basal ganglia and thalamus.

@entity1032 @entity932 @entity410 @entity146 @entity1269 @entity428 @entity5 @entity2554 @entity194 @entity3438 @entity2010
Clinical characteristics of six cases of @entity3438 involving a unilateral basal ganglion and thalamus are summarized. The incidence was estimated as 10% of all @entity932 . The average age at the onset was 10.5 years. The sex incidence showed a male dominance. The clinical course was slowly progressive, and the average duration between onset and diagnosis was 2 years 5 months. Common symptoms and signs were @entity1269 in all cases, fever of unknown origin and eye symptoms in most, @entity1032 and @entity146 signs in three, and @entity410 , pubertas praecox, and @entity2010 in two. Signs of @entity428 were found in only two cases in the later state of the disease. Early diagnosis is difficult because of nonspecific symptomatology and slow progression. Carotid angiography and pneumoencephalography showed abnormal findings compatible with basal @entity5 , but not specific to @entity3438 . Ipsilateral cortical @entity194 and @entity2554 might be significant findings. Radioisotope scanning was useful. Computerized tomography scans were the best method of detecting the location and nature of this @entity5 , and repeat scans showed response to radiation therapy.
