Occlusive hydrocephalus complicating XXXX : report of two cases.

@entity1 @entity410 @entity428 @entity5 @entity75 @entity2916 @entity816
Two @entity1 -6 and 14 years old-with @entity2916 are presented. Both developed a @entity816 from nodules located near to the foramen of Monro. They caused obstruction of the cerebrospinal fluid pathways. Signs of @entity428 were detected in both @entity1 , and one of them had also developed @entity410 . Cutaneous stigmata being characteristic for this entity were observed in both cases, but their mental development was unaffected. Diagnosis was based on computed tomography. Angiography did not reveal pathological vessels. The @entity5 were completely excised through transcallosal exposure in both cases. The @entity1 have been symptom-free during the follow-up time of 1 and 2 years. Although the incidence of malignant transformation of @entity2916 is less than 15% the disease generally has a poor prognosis which can be ascribed to sudden increase of intracranial pressure caused by obstruction of cerebrospinal fluid pathways by paraventricular @entity5 . However, regular follow-up of paraventricular nodules and maintenance of patency of cerebrospinal fluid pathways by microsurgical methods in @entity1 suffering from mild @entity75 offers a better chance of survival.
