Symptomatic XXXX : clinico-radiological analysis in a series of eight operative cases with follow-up results.

@entity1 @entity227 @entity82 @entity7994 @entity75 @entity2694 @entity79 @entity7577 @entity10 @entity393 @entity4838 @entity85
Cranial @entity82 are rare and comprise less than one percent of all primary @entity79 . These painless progressively expanding destructive @entity79 produce @entity85 (commonest), @entity2694 (less common), peripheral @entity7577 (uncommon) and compressive central neurological manifestations (rarest). Until recently some of the primary @entity75 were either treated expectantly or excised incompletely. In a significant percentage of cases, these lesions were considered inaccessible. However, with the development of modern neuro-imaging ( @entity7994 ) and the applications of current skull base approaches, the more aggressive and radical surgical procedures are being undertaken, with a significant improvement in overall outcome. We present a series of 8 cases of @entity82 in the age group of 10-33 years with a mean age of 19.75 years. Four cases each had monostotic type and polyostotic type. All @entity1 presented with mild to moderate @entity10 , and seven cases with some form of @entity85 . In 4 @entity1 there was a unilateral proptosis, while only two had @entity227 . One @entity1 had @entity4838 and one @entity393 . In one case @entity82 was hemicranial, and in another case the disease was pancranial. Neuro-imaging studies have well delineated the extent of the lesions. In two @entity1 with @entity2694 , the removal of dysplastic bone, autoclaving and remodeling and replacement were performed. In two @entity1 of sphenoidal wing @entity82 a total excision was possible. In the remaining four @entity1 , a partial excision was performed. Overall outcome was good. There was no mortality. One @entity1 had recurrent post-operative extradural haematomas. The authors present the results of an analysis of eight surgically treated cases of symptomatic @entity82 along with their long-term outcome and the lessons learnt from this series.
