Malignant XXXX associated with diaphyseal medullary stenosis.

@entity1 @entity2835 @entity82 @entity7195 @entity242 @entity5 @entity49517 @entity79 @entity1188
An unusual presentation of secondary malignant @entity82 of the femur in a @entity1 with diaphyseal medullary stenosis is described. The @entity1 , a 42-year-old @entity1 , presented with a painful lump in the right knee. A radiograph of the right femur showed @entity2835 . Characteristic features of @entity49517 in the metaphysis and medullary stenosis in the diaphysis were observed in radiographs of the long tubular bones. A radiograph of the pelvis showed bilateral acetabular bone scleroses. After chemotherapy, surgical resection was done. On light microscopic examination, the @entity5 had features characteristic of malignant @entity82 . Specimens from the diaphyseal medullary stenosis from the femur and tibia showed typical features of @entity1188 . Radiographs of other members of the @entity1 's family showed similar features of linear striation, cortical bone thickening, and @entity7195 , including wavy, open growth plate of the iliac crest. The @entity1 's aunt had died of a @entity79 in the shoulder region. It is important to recognize this extremely rare clinicopathologic type of diaphyseal medullary stenosis that frequently is associated with secondary high-grade @entity242 .
