[Vasculo-Beh  et's disease with XXXX --case report (author's transl)].

@entity1 @entity32 @entity227 @entity1066 @entity2268 @entity5389 @entity134 @entity4754 @entity272 @entity432 @entity715 @entity10 @entity50 @entity5406
The @entity1 is a 30-year-old @entity1 who has suffered from recurrent @entity5389 , oral aphthae and scrotal @entity1066 , @entity5406 and @entity2268 . In April, 1980, he gradually developed @entity10 and @entity227 . On April 14, 1980, he was pointed out remarked bilateral choked disc by an ophthalmologist and then admitted to the Miyazaki Medical College Hospital. On admission to our service, he showed atypical symptoms of Beh  et's disease, namely, oral aphthae and scrotal @entity1066 , @entity5406 and bilateral choked disc. Laboratory data demonstrated @entity4754 , increased clotting factors and decreased fibrinolytic activity. Immunogenetically, HLA BW51 type was demonstrated. The angiograms showed @entity432 . Histological examination of the @entity272 demonstrated @entity32 and @entity2268 . A diagnosis of atypical Vasculo-Beh  et's disease was made. The response to the @entity134 therapy was dramatic, though the fibrinolytic drugs, anticoagulants and vasodilators were not effective. @entity2268 is a well recognized complication of Beh  et's disease occurring in major vessels, however @entity715 of the dural sinus has rarely reported. This case may be the first one which had @entity50 with Vasculo-Beh  et's disease in literature. We discussed the mechanism of the thrombogenesis, the relationship to HLA, the coexistence of Neuro-Beh  et's disease and the therapy of Vasculo-Beh  et's disease.
