Idiopathic dilated XXXX : a report of eight cases.

@entity1 @entity712 @entity1165 @entity296 @entity2554 @entity854 @entity1001 @entity67 @entity943 @entity1002
From 1970 to 1983, eight @entity1 who had severe right @entity2554 with little or no @entity1002 were referred to our hospital. There were two @entity1 and six @entity1 , whose ages ranged from 16 to 38 years and averaged 27. Five @entity1 were members of two families, which had definite hereditary histories of this disease. ECGs of seven @entity1 suggested right @entity67 . @entity943 were documented in seven, whose ECGs suggested that the origins of the @entity943 were in the right or both ventricles. Cardiothoracic ratios ranged from 0.50 to 0.66 and averaged 0.59. Five @entity1 had wide respiratory splitting of the second heart sound. Echocardiography showed a marked increase in the right ventricular dimension. Right ventricular diastolic pressure was increased in three; left ventricular diastolic pressure was increased in two. Right ventricular angiography revealed marked dilatation and low ejection fractions of the right ventricle in all, but left ventricular function was nearly normal in them, except two @entity1 who had minimal abnormality. The average follow-up period was 6.3 years and ranged from 3 months to 11 years. During the follow-up period, only two @entity1 had @entity1165 and three developed overt @entity712 . Three @entity1 died, two suddenly, and one from an attack of @entity1165 . Autopsies of these two showed extreme dilatation of the right ventricle and one of them showed concentric hypertrophy of the left ventricle. @entity854 were found in both ventricles. In summary, it is suggested that idiopathic dilated @entity1001 can be classified in the spectrum of dilated @entity296 .
