XXXX with @entity438 : a case report.

@entity1 @entity64 @entity101 @entity384 @entity117 @entity1163 @entity9886 @entity887 @entity453 @entity33790 @entity616 @entity438
OBJECTIVE: To report a new manifestation of the rare connective tissue disorder @entity33790 in the absence of skin and soft-tissue abnormalities and with bilateral, giant fusiform @entity438 . DESIGN: Case report. SETTING: University teaching hospital. @entity1 : A 67-year-old @entity1 with a history of @entity101 presented to medical attention after a @entity1163 . Imaging revealed incidental, bilateral, giant fusiform @entity438 at their junction of the circle of Willis. There was also @entity384 of the left main @entity453 and @entity384 of the aorta and bilateral iliac arteries, suggestive of @entity33790 . RESULTS: The @entity1 's @entity1163 was attributed to transient complete @entity616 for which a permanent pacemaker was placed. The @entity1 started taking @entity117 for @entity64 prevention and @entity9886 for blood pressure control. CONCLUSIONS: To our knowledge, we present the first case of @entity33790 with marked bilateral intracranial artery dilation in the absence of concurrent skin and soft tissue abnormalities. Workup may include systemic vascular imaging to characterize the extent of disease. Antiplatelet therapy can be used for @entity64 prevention by reducing the risk of clot formation in ectatic vessels with altered hemodynamics and subsequent @entity887 . @entity9886 is known to inhibit transforming growth factor b signaling and may be a specific modulator of disease expression in this syndrome.
