Renal manifestations of XXXX complex.

@entity1 @entity8 @entity5 @entity16 @entity812 @entity4848 @entity2916 @entity1358 @entity158 @entity359 @entity811 @entity204
@entity2916 ( @entity2916 ) is an autosomal-dominant @entity4848 involving the skin, brain, kidney, heart and other organs. Renal manifestations are @entity359 , @entity8 and @entity5 . We report three female @entity1 , mean aged of 31 years (range: 22-37), with a family history of @entity2916 in one case. @entity16 were found in all @entity1 . Clinical complaints were mainly abdominal @entity158 (3 cases), @entity811 (2 cases), right flank palpable mass (1 case). @entity359 ( @entity359 ) were diagnosed by ultrasonography in all @entity1 , associated to @entity8 in one case. A @entity1 underwent total right nephrectomy without any event during the follow-up. In a second @entity1 , a selective arterial embolization of @entity359 was indicated. Total left nephrectomy was performed due to the persistence of @entity811 and the @entity812 . Pathological examination of the kidney revealed @entity1358 . The third @entity1 with small @entity359 , associated with @entity8 , required careful monitoring. Renal manifestations in @entity2916 are frequent and serious, they are the second leading cause of @entity204 after nervous lesions. Clinical and morphological aspects are variable and different therapeutic indications must be discussed.
