Updates in adult-onset Still disease: Atypical cutaneous manifestations and associations with delayed XXXX .

@entity1 @entity32 @entity11533 @entity0 @entity5 @entity272 @entity8231
UNASSIGNED: @entity11533 ( @entity11533 ) is a systemic @entity32 that is clinically characterized by a heterogeneous constellation of symptoms and signs. Though an evanescent eruption is the classic cutaneous finding, recent literature has highlighted atypical rashes associated with Still disease. A second emerging concept in presentations of @entity11533 is its association with @entity5 . This review focuses on these concepts: the clinical spectrum of atypical skin manifestations and @entity11533 as a @entity8231 phenomenon. PubMed-MEDLINE was screened for peer-reviewed articles describing atypical presentations of @entity11533 and cases associated with @entity5 . Erythematous, brown or violaceous, persistent papules and plaques were the most common cutaneous finding (28/30 [93%]). Linear configurations were also rarely described. Of these @entity1 , 81% concurrently had the typical evanescent @entity272 . There were 31 @entity1 with associated @entity5 , most commonly @entity0 . The diagnosis of @entity5 did not precede or immediately follow a clinical presentation otherwise consistent with @entity11533 in a considerable subset of @entity1 (42%). Understanding the cutaneous spectrum of @entity11533 and heightened awareness for its delayed association with @entity5 may lead to improved recognition of cutaneous variants and reinforce the need for diagnostic evaluation and long-term follow-up for @entity5 in @entity1 with this clinical presentation.
