@entity79 associated with XXXX in @entity10244 .

@entity1 @entity10244 @entity8468 @entity509 @entity79 @entity15902 @entity1274 @entity389 @entity62830 @entity393
OBJECTIVES/HYPOTHESIS: The objectives were to correlate audiometric thresholds with radiological findings and to determine the prevalence of @entity389 in @entity1 with @entity393 and @entity10244 . STUDY DESIGN: The study was a retrospective review of @entity1 with @entity10244 identified in a pediatric hearing-impaired population and @entity1 genetics clinic. METHODS: Nine @entity1 with @entity10244 were identified. Eighty-nine @entity1 without @entity1274 served as control subjects. Clinical data, audiometric thresholds, and radiographic temporal bone measurements in these @entity1 were analyzed. RESULTS: Seven @entity1 were identified with @entity393 and @entity10244 . Four @entity1 had @entity10244 , and three @entity1 had @entity62830 . The overall prevalence of @entity393 in the total study population with @entity10244 was 78%. The mean pure-tone average was 99 dB. All of the @entity1 had @entity1274 . The hearing outcome was stable in 86% of the @entity1 . Twelve temporal bones were available for radiological analysis by computed tomography. Enlargement of the @entity8468 was found in 50% of the CT scans. There was a significant difference in measurements of @entity8468 width at the midpoint between the @entity1 with @entity10244 and the control group (P <.05). There were also significant differences in the measurements of the vestibule (P =.0484), internal auditory canal (P =.0092), and modiolus (P =.0045) between the @entity1 with @entity10244 and the control group. CONCLUSION: A profound @entity1274 was characteristic of the study population with @entity10244 . Overall, 100% of @entity1 with @entity393 and @entity10244 had @entity79 on at least one measurement of their inner ear, and 50% had an @entity15902 at the midpoint. As shown by computed tomography, @entity15902 and the upper vestibule, narrowing of the internal auditory canal porus, and @entity509 of the modiolus are features of @entity10244 .
